ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 17  /  Q80-Q89  /  Q89
Q89 Other congenital malformations, not elsewhere classified
Q89.0 Congenital absence and malformations of spleen
Excludes1 isomerism of atrial appendages (with asplenia or polysplenia) (Q20.6)
Q89.01 Asplenia (congenital)
Q89.09 Congenital malformations of spleen
Congenital splenomegaly
Q89.1 Congenital malformations of adrenal gland
Excludes1 adrenogenital disorders (E25.-)
congenital adrenal hyperplasia (E25.0)
Q89.2 Congenital malformations of other endocrine glands
Congenital malformation of parathyroid or thyroid gland
Persistent thyroglossal duct
Thyroglossal cyst
Excludes1 congenital goiter (E03.0)
congenital hypothyroidism (E03.1)
Q89.3 Situs inversus
Dextrocardia with situs inversus
Mirror-image atrial arrangement with situs inversus
Situs inversus or transversus abdominalis
Situs inversus or transversus thoracis
Transposition of abdominal viscera
Transposition of thoracic viscera
Excludes1 dextrocardia NOS (Q24.0)
Q89.4 Conjoined twins
Craniopagus
Dicephaly
Pygopagus
Thoracopagus
Q89.7 Multiple congenital malformations, not elsewhere classified
Multiple congenital anomalies NOS
Multiple congenital deformities NOS
Excludes1 congenital malformation syndromes affecting multiple systems (Q87.-)
Q89.8 Other specified congenital malformations
UseAdditionalCode code(s) to identify all associated manifestations
Q89.9 Congenital malformation, unspecified
Congenital anomaly NOS
Congenital deformity NOS