|  C91 |  | Lymphoid leukemia   | 
	
		|  |  | 
	
		| Excludes1 | personal history of leukemia (Z85.6) 
 |  | 
|  |  | 
	
		|  C91.0 |  | Acute lymphoblastic leukemia [ALL] |  
		|  |  | 
	
		| Notes | Codes in subcategory C91.0- should only be used for T-cell and B-cell precursor leukemia 
 |  |  |  |  | 
	
		|  C91.00 |  | Acute lymphoblastic leukemia not having achieved remission |  
		|  |  | 
| Acute lymphoblastic leukemia with failed remission |  | Acute lymphoblastic leukemia NOS |  |  |  |  |  | 
	
		|  C91.01 |  | Acute lymphoblastic leukemia, in remission |  |  |  |  | 
	
		|  C91.02 |  | Acute lymphoblastic leukemia, in relapse |  |  | 
|  |  | 
	
		|  C91.1 |  | Chronic lymphocytic leukemia of B-cell type |  
		|  |  | 
| Lymphoplasmacytic leukemia |  | Richter syndrome |  
		| Excludes1 | lymphoplasmacytic lymphoma (C83.0-) 
 |  |  |  |  | 
	
		|  C91.10 |  | Chronic lymphocytic leukemia of B-cell type not having achieved remission |  
		|  |  | 
| Chronic lymphocytic leukemia of B-cell type with failed remission |  | Chronic lymphocytic leukemia of B-cell type NOS |  |  |  |  |  | 
	
		|  C91.11 |  | Chronic lymphocytic leukemia of B-cell type in remission |  |  |  |  | 
	
		|  C91.12 |  | Chronic lymphocytic leukemia of B-cell type in relapse |  |  | 
|  |  | 
	
		|  C91.3 |  | Prolymphocytic leukemia of B-cell type |  |  |  | 
	
		|  C91.30 |  | Prolymphocytic leukemia of B-cell type not having achieved remission |  
		|  |  | 
| Prolymphocytic leukemia of B-cell type with failed remission |  | Prolymphocytic leukemia of B-cell type NOS |  |  |  |  |  | 
	
		|  C91.31 |  | Prolymphocytic leukemia of B-cell type, in remission |  |  |  |  | 
	
		|  C91.32 |  | Prolymphocytic leukemia of B-cell type, in relapse |  |  | 
|  |  | 
	
		|  C91.4 |  | Hairy cell leukemia |  
		|  |  | 
| Leukemic reticuloendotheliosis |  |  |  |  | 
	
		|  C91.40 |  | Hairy cell leukemia not having achieved remission |  
		|  |  | 
| Hairy cell leukemia with failed remission |  | Hairy cell leukemia NOS |  |  |  |  |  | 
	
		|  C91.41 |  | Hairy cell leukemia, in remission |  |  |  |  | 
	
		|  C91.42 |  | Hairy cell leukemia, in relapse |  |  | 
|  |  | 
	
		|  C91.5 |  | Adult T-cell lymphoma/leukemia (HTLV-1-associated) |  
		|  |  | 
| Acute variant of adult T-cell lymphoma/leukemia (HTLV-1-associated) |  | Chronic variant of adult T-cell lymphoma/leukemia (HTLV-1-associated) |  | Lymphomatoid variant of adult T-cell lymphoma/leukemia (HTLV-1-associated) |  | Smouldering variant of adult T-cell lymphoma/leukemia (HTLV-1-associated) |  |  |  |  | 
	
		|  C91.50 |  | Adult T-cell lymphoma/leukemia (HTLV-1-associated) not having achieved remission |  
		|  |  | 
| Adult T-cell lymphoma/leukemia (HTLV-1-associated) with failed remission |  | Adult T-cell lymphoma/leukemia (HTLV-1-associated) NOS |  
		| age | Adult: [15-124] 
 |  |  |  |  |  | 
	
		|  C91.51 |  | Adult T-cell lymphoma/leukemia (HTLV-1-associated), in remission |  
		|  |  |  |  |  |  |  | 
	
		|  C91.52 |  | Adult T-cell lymphoma/leukemia (HTLV-1-associated), in relapse |  
		|  |  |  |  |  | 
|  |  | 
	
		|  C91.6 |  | Prolymphocytic leukemia of T-cell type |  |  |  | 
	
		|  C91.60 |  | Prolymphocytic leukemia of T-cell type not having achieved remission |  
		|  |  | 
| Prolymphocytic leukemia of T-cell type with failed remission |  | Prolymphocytic leukemia of T-cell type NOS |  |  |  |  |  | 
	
		|  C91.61 |  | Prolymphocytic leukemia of T-cell type, in remission |  |  |  |  | 
	
		|  C91.62 |  | Prolymphocytic leukemia of T-cell type, in relapse |  |  | 
|  |  | 
	
		|  C91.A |  | Mature B-cell leukemia Burkitt-type |  
		|  |  | 
	
		| Excludes1 | Burkitt lymphoma (C83.7-) 
 |  |  |  |  | 
	
		|  C91.A0 |  | Mature B-cell leukemia Burkitt-type not having achieved remission |  
		|  |  | 
| Mature B-cell leukemia Burkitt-type with failed remission |  | Mature B-cell leukemia Burkitt-type NOS |  |  |  |  |  | 
	
		|  C91.A1 |  | Mature B-cell leukemia Burkitt-type, in remission |  |  |  |  | 
	
		|  C91.A2 |  | Mature B-cell leukemia Burkitt-type, in relapse |  |  | 
|  |  | 
	
		|  C91.Z |  | Other lymphoid leukemia |  
		|  |  | 
| T-cell large granular lymphocytic leukemia (associated with rheumatoid arthritis) |  |  |  |  | 
	
		|  C91.Z0 |  | Other lymphoid leukemia not having achieved remission |  
		|  |  | 
| Other lymphoid leukemia with failed remission |  | Other lymphoid leukemia NOS |  |  |  |  |  | 
	
		|  C91.Z1 |  | Other lymphoid leukemia, in remission |  |  |  |  | 
	
		|  C91.Z2 |  | Other lymphoid leukemia, in relapse |  |  | 
|  |  | 
	
		|  C91.9 |  | Lymphoid leukemia, unspecified |  |  |  | 
	
		|  C91.90 |  | Lymphoid leukemia, unspecified not having achieved remission |  
		|  |  | 
| Lymphoid leukemia with failed remission |  | Lymphoid leukemia NOS |  |  |  |  |  | 
	
		|  C91.91 |  | Lymphoid leukemia, unspecified, in remission |  |  |  |  | 
	
		|  C91.92 |  | Lymphoid leukemia, unspecified, in relapse |  |  |