ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 3  /  D55-D59  /  D55
D55 Anemia due to enzyme disorders
Excludes1 drug-induced enzyme deficiency anemia (D59.2)
D55.0 Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency
Favism
G6PD deficiency anemia
Excludes1 glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia (D75.A)
D55.1 Anemia due to other disorders of glutathione metabolism
Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway
Anemia (due to) hemolytic nonspherocytic (hereditary), type I
D55.2 Anemia due to disorders of glycolytic enzymes
Excludes1 disorders of glycolysis not associated with anemia (E74.81-)
D55.21 Anemia due to pyruvate kinase deficiency
PK deficiency anemia
Pyruvate kinase deficiency anemia
D55.29 Anemia due to other disorders of glycolytic enzymes
Hexokinase deficiency anemia
Triose-phosphate isomerase deficiency anemia
D55.3 Anemia due to disorders of nucleotide metabolism
D55.8 Other anemias due to enzyme disorders
D55.9 Anemia due to enzyme disorder, unspecified