|  D55 |  | Anemia due to enzyme disorders   | 
	
		|  |  | 
	
		| Excludes1 | drug-induced enzyme deficiency anemia (D59.2) 
 |  | 
|  |  | 
	
		|  D55.0 |  | Anemia due to glucose-6-phosphate dehydrogenase [G6PD] deficiency |  
		|  |  | 
| Favism |  | G6PD deficiency anemia |  
		| Excludes1 | glucose-6-phosphate dehydrogenase (G6PD) deficiency without anemia (D75.A) 
 |  |  | 
|  |  | 
	
		|  D55.1 |  | Anemia due to other disorders of glutathione metabolism |  
		|  |  | 
| Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway |  | Anemia (due to) hemolytic nonspherocytic (hereditary), type I |  |  | 
|  |  | 
	
		|  D55.2 |  | Anemia due to disorders of glycolytic enzymes |  
		|  |  | 
	
		| Excludes1 | disorders of glycolysis not associated with anemia (E74.81-) 
 |  |  |  |  | 
	
		|  D55.21 |  | Anemia due to pyruvate kinase deficiency |  
		|  |  | 
| PK deficiency anemia |  | Pyruvate kinase deficiency anemia |  |  |  |  |  | 
	
		|  D55.29 |  | Anemia due to other disorders of glycolytic enzymes |  
		|  |  | 
| Hexokinase deficiency anemia |  | Triose-phosphate isomerase deficiency anemia |  |  |  | 
|  |  | 
	
		|  D55.3 |  | Anemia due to disorders of nucleotide metabolism |  | 
|  |  | 
	
		|  D55.8 |  | Other anemias due to enzyme disorders |  | 
|  |  | 
	
		|  D55.9 |  | Anemia due to enzyme disorder, unspecified |  |