ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 3  /  D55-D59  /  D57
D57 Sickle-cell disorders
UseAdditionalCode code for any associated fever (R50.81)
Excludes1 other hemoglobinopathies (D58.-)
D57.0 Hb-SS disease with crisis
Sickle-cell disease with crisis
Hb-SS disease with (vaso-occlusive) pain
D57.00 Hb-SS disease with crisis, unspecified
Hb-SS disease with (painful) crisis NOS
Hb-SS disease with (vaso-occlusive) pain NOS
D57.01 Hb-SS disease with acute chest syndrome
D57.02 Hb-SS disease with splenic sequestration
D57.03 Hb-SS disease with cerebral vascular involvement
CodeAlso , if applicable, cerebral infarction (I63.-)
D57.04 Hb-SS disease with dactylitis
D57.09 Hb-SS disease with crisis with other specified complication
UseAdditionalCode code to identify complications, such as:
cholelithiasis (K80.-)
priapism (N48.32)
D57.1 Sickle-cell disease without crisis
Hb-SS disease without crisis
Sickle-cell anemia NOS
Sickle-cell disease NOS
Sickle-cell disorder NOS
D57.2 Sickle-cell/Hb-C disease
Hb-SC disease
Hb-S/Hb-C disease
D57.20 Sickle-cell/Hb-C disease without crisis
D57.21 Sickle-cell/Hb-C disease with crisis
D57.211 Sickle-cell/Hb-C disease with acute chest syndrome
D57.212 Sickle-cell/Hb-C disease with splenic sequestration
D57.213 Sickle-cell/Hb-C disease with cerebral vascular involvement
CodeAlso , if applicable, cerebral infarction (I63.-)
D57.214 Sickle-cell/Hb-C disease with dactylitis
D57.218 Sickle-cell/Hb-C disease with crisis with other specified complication
UseAdditionalCode code to identify complications, such as:
cholelithiasis (K80.-)
priapism (N48.32)
D57.219 Sickle-cell/Hb-C disease with crisis, unspecified
Sickle-cell/Hb-C disease with crisis NOS
Sickle-cell/Hb-C disease with (vaso-occlusive) pain NOS
D57.3 Sickle-cell trait
Hb-S trait
Heterozygous hemoglobin S
D57.4 Sickle-cell thalassemia
Sickle-cell beta thalassemia
Thalassemia Hb-S disease
D57.40 Sickle-cell thalassemia without crisis
Microdrepanocytosis
Sickle-cell thalassemia NOS
D57.41 Sickle-cell thalassemia, unspecified, with crisis
Sickle-cell thalassemia with (painful) crisis NOS
Sickle-cell thalassemia with (vaso-occlusive) pain NOS
D57.411 Sickle-cell thalassemia, unspecified, with acute chest syndrome
D57.412 Sickle-cell thalassemia, unspecified, with splenic sequestration
D57.413 Sickle-cell thalassemia, unspecified, with cerebral vascular involvement
CodeAlso , if applicable cerebral infarction (I63.-)
D57.414 Sickle-cell thalassemia, unspecified, with dactylitis
D57.418 Sickle-cell thalassemia, unspecified, with crisis with other specified complication
UseAdditionalCode code to identify complications, such as:
cholelithiasis (K80.-)
priapism (N48.32)
D57.419 Sickle-cell thalassemia, unspecified, with crisis
Sickle-cell thalassemia with (painful) crisis NOS
Sickle-cell thalassemia with (vaso-occlusive) pain NOS
D57.42 Sickle-cell thalassemia beta zero without crisis
HbS-beta zero without crisis
Sickle-cell beta zero without crisis
D57.43 Sickle-cell thalassemia beta zero with crisis
HbS-beta zero with crisis
Sickle-cell beta zero with crisis
D57.431 Sickle-cell thalassemia beta zero with acute chest syndrome
HbS-beta zero with acute chest syndrome
Sickle-cell beta zero with acute chest syndrome
D57.432 Sickle-cell thalassemia beta zero with splenic sequestration
HbS-beta zero with splenic sequestration
Sickle-cell beta zero with splenic sequestration
D57.433 Sickle-cell thalassemia beta zero with cerebral vascular involvement
HbS-beta zero with cerebral vascular involvement
Sickle-cell beta zero with cerebral vascular involvement
CodeAlso , if applicable cerebral infarction (I63.-)
D57.434 Sickle-cell thalassemia beta zero with dactylitis
D57.438 Sickle-cell thalassemia beta zero with crisis with other specified complication
HbS-beta zero with other specified complication
Sickle-cell beta zero with other specified complication
UseAdditionalCode code to identify complications, such as:
cholelithiasis (K80.-)
priapism (N48.32)
D57.439 Sickle-cell thalassemia beta zero with crisis, unspecified
HbS-beta zero with other specified complication
Sickle-cell beta zero with crisis unspecified
Sickle-cell thalassemia beta zero with (painful) crisis NOS
Sickle-cell thalassemia beta zero with (vaso-occlusive) pain NOS
D57.44 Sickle-cell thalassemia beta plus without crisis
HbS-beta plus without crisis
Sickle-cell beta plus without crisis
D57.45 Sickle-cell thalassemia beta plus with crisis
HbS-beta plus with crisis
Sickle-cell beta plus with crisis
D57.451 Sickle-cell thalassemia beta plus with acute chest syndrome
HbS-beta plus with acute chest syndrome
Sickle-cell beta plus with acute chest syndrome
D57.452 Sickle-cell thalassemia beta plus with splenic sequestration
HbS-beta plus with splenic sequestration
Sickle-cell beta plus with splenic sequestration
D57.453 Sickle-cell thalassemia beta plus with cerebral vascular involvement
HbS-beta plus with cerebral vascular involvement
Sickle-cell beta plus with cerebral vascular involvement
CodeAlso , if applicable cerebral infarction (I63.-)
D57.454 Sickle-cell thalassemia beta plus with dactylitis
D57.458 Sickle-cell thalassemia beta plus with crisis with other specified complication
HbS-beta plus with crisis with other specified complication
Sickle-cell beta plus with crisis with other specified complication
UseAdditionalCode code to identify complications, such as:
cholelithiasis (K80.-)
priapism (N48.32)
D57.459 Sickle-cell thalassemia beta plus with crisis, unspecified
HbS-beta plus with crisis with unspecified complication
Sickle-cell beta plus with crisis with unspecified complication
Sickle-cell thalassemia beta plus with (painful) crisis NOS
Sickle-cell thalassemia beta plus with (vaso-occlusive) pain NOS
D57.8 Other sickle-cell disorders
Hb-SD disease
Hb-SE disease
D57.80 Other sickle-cell disorders without crisis
D57.81 Other sickle-cell disorders with crisis
D57.811 Other sickle-cell disorders with acute chest syndrome
D57.812 Other sickle-cell disorders with splenic sequestration
D57.813 Other sickle-cell disorders with cerebral vascular involvement
CodeAlso , if applicable: cerebral infarction (I63.-)
D57.814 Other sickle-cell disorders with dactylitis
D57.818 Other sickle-cell disorders with crisis with other specified complication
UseAdditionalCode code to identify complications, such as:
cholelithiasis (K80.-)
priapism (N48.32)
D57.819 Other sickle-cell disorders with crisis, unspecified
Other sickle-cell disorders with crisis NOS
Other sickle-cell disorders with (vaso-occlusive) pain NOS