E76 |
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Disorders of glycosaminoglycan metabolism  |
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E76.0 |
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Mucopolysaccharidosis, type I |
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E76.01 |
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Hurler's syndrome |
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E76.02 |
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Hurler-Scheie syndrome |
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E76.03 |
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Scheie's syndrome |
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E76.1 |
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Mucopolysaccharidosis, type II |
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E76.2 |
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Other mucopolysaccharidoses |
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E76.21 |
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Morquio mucopolysaccharidoses |
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E76.210 |
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Morquio A mucopolysaccharidoses |
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| Classic Morquio syndrome | | Morquio syndrome A | | Mucopolysaccharidosis, type IVA |
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E76.211 |
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Morquio B mucopolysaccharidoses |
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| Morquio-like mucopolysaccharidoses | | Morquio-like syndrome | | Morquio syndrome B | | Mucopolysaccharidosis, type IVB |
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E76.219 |
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Morquio mucopolysaccharidoses, unspecified |
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| Morquio syndrome | | Mucopolysaccharidosis, type IV |
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E76.22 |
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Sanfilippo mucopolysaccharidoses |
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| Mucopolysaccharidosis, type III (A) (B) (C) (D) | | Sanfilippo A syndrome | | Sanfilippo B syndrome | | Sanfilippo C syndrome | | Sanfilippo D syndrome |
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E76.29 |
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Other mucopolysaccharidoses |
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| beta-Glucuronidase deficiency | | Maroteaux-Lamy (mild) (severe) syndrome | | Mucopolysaccharidosis, types VI, VII |
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E76.3 |
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Mucopolysaccharidosis, unspecified |
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E76.8 |
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Other disorders of glucosaminoglycan metabolism |
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E76.9 |
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Glucosaminoglycan metabolism disorder, unspecified |
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