ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 4  /  E70-E88  /  E76
E76 Disorders of glycosaminoglycan metabolism
E76.0 Mucopolysaccharidosis, type I
E76.01 Hurler's syndrome
E76.02 Hurler-Scheie syndrome
E76.03 Scheie's syndrome
E76.1 Mucopolysaccharidosis, type II
Hunter's syndrome
E76.2 Other mucopolysaccharidoses
E76.21 Morquio mucopolysaccharidoses
E76.210 Morquio A mucopolysaccharidoses
Classic Morquio syndrome
Morquio syndrome A
Mucopolysaccharidosis, type IVA
E76.211 Morquio B mucopolysaccharidoses
Morquio-like mucopolysaccharidoses
Morquio-like syndrome
Morquio syndrome B
Mucopolysaccharidosis, type IVB
E76.219 Morquio mucopolysaccharidoses, unspecified
Morquio syndrome
Mucopolysaccharidosis, type IV
E76.22 Sanfilippo mucopolysaccharidoses
Mucopolysaccharidosis, type III (A) (B) (C) (D)
Sanfilippo A syndrome
Sanfilippo B syndrome
Sanfilippo C syndrome
Sanfilippo D syndrome
E76.29 Other mucopolysaccharidoses
beta-Glucuronidase deficiency
Maroteaux-Lamy (mild) (severe) syndrome
Mucopolysaccharidosis, types VI, VII
E76.3 Mucopolysaccharidosis, unspecified
E76.8 Other disorders of glucosaminoglycan metabolism
E76.9 Glucosaminoglycan metabolism disorder, unspecified