ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 9  /  I26-I28  /  I27
I27 Other pulmonary heart diseases
I27.0 Primary pulmonary hypertension
Heritable pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension
Primary group 1 pulmonary hypertension
Primary pulmonary arterial hypertension
Excludes1 persistent pulmonary hypertension of newborn (P29.30)
pulmonary hypertension NOS (I27.20)
secondary pulmonary arterial hypertension (I27.21)
secondary pulmonary hypertension (I27.29)
I27.1 Kyphoscoliotic heart disease
I27.2 Other secondary pulmonary hypertension
CodeAlso associated underlying condition
Excludes1 Eisenmenger's syndrome (I27.83)
I27.20 Pulmonary hypertension, unspecified
Pulmonary hypertension NOS
I27.21 Secondary pulmonary arterial hypertension
(Associated) (drug-induced) (toxin-induced) pulmonary arterial hypertension NOS
(Associated) (drug-induced) (toxin-induced) (secondary) group 1 pulmonary hypertension
CodeAlso associated conditions if applicable, or adverse effects of drugs or toxins, such as:
adverse effect of appetite depressants (T50.5X5)
congenital heart disease (Q20-Q28)
human immunodeficiency virus [HIV] disease (B20)
polymyositis (M33.2-)
portal hypertension (K76.6)
rheumatoid arthritis (M05.-)
schistosomiasis (B65.-)
Sjögren syndrome (M35.0-)
systemic sclerosis (M34.-)
I27.22 Pulmonary hypertension due to left heart disease
Group 2 pulmonary hypertension
CodeAlso associated left heart disease, if known, such as:
multiple valve disease (I08.-)
rheumatic mitral valve diseases (I05.-)
rheumatic aortic valve diseases (I06.-)
I27.23 Pulmonary hypertension due to lung diseases and hypoxia
Group 3 pulmonary hypertension
CodeAlso associated lung disease, if known, such as:
bronchiectasis (J47.-)
cystic fibrosis with pulmonary manifestations (E84.0)
interstitial lung disease (J84.-)
pleural effusion (J90)
sleep apnea (G47.3-)
I27.24 Chronic thromboembolic pulmonary hypertension
Group 4 pulmonary hypertension
CodeAlso associated pulmonary embolism, if applicable (I26.-, I27.82)
I27.29 Other secondary pulmonary hypertension
Group 5 pulmonary hypertension
Pulmonary hypertension with unclear multifactorial mechanisms
Pulmonary hypertension due to hematologic disorders
Pulmonary hypertension due to metabolic disorders
Pulmonary hypertension due to other systemic disorders
CodeAlso other associated disorders, if known, such as:
chronic myeloid leukemia (C92.10-C92.22)
essential thrombocythemia (D47.3)
Gaucher disease (E75.22)
hypertensive chronic kidney disease with end stage renal disease (I12.0, I13.11, I13.2)
hyperthyroidism (E05.-)
hypothyroidism (E00-E03)
polycythemia vera (D45)
sarcoidosis (D86.-)
I27.8 Other specified pulmonary heart diseases
I27.81 Cor pulmonale (chronic)
Cor pulmonale NOS
CodeAlso , if applicable, right heart failure (I50.81-)
Excludes1 acute cor pulmonale (I26.0-)
I27.82 Chronic pulmonary embolism
UseAdditionalCode code, if applicable, for associated long-term (current) use of anticoagulants (Z79.01)
Excludes1 personal history of pulmonary embolism (Z86.711)
I27.83 Eisenmenger's syndrome
Eisenmenger's complex
(Irreversible) Eisenmenger's disease
Pulmonary hypertension with right to left shunt related to congenital heart disease
CodeAlso underlying heart defect, if known, such as:
atrial septal defect (Q21.1-)
Eisenmenger's defect (Q21.8)
patent ductus arteriosus (Q25.0)
ventricular septal defect (Q21.0)
I27.89 Other specified pulmonary heart diseases
I27.9 Pulmonary heart disease, unspecified
Chronic cardiopulmonary disease