ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 17  /  Q00-Q07  /  Q04
Q04 Other congenital malformations of brain
Excludes1 cyclopia (Q87.0)
macrocephaly (Q75.3)
Q04.0 Congenital malformations of corpus callosum
Agenesis of corpus callosum
Q04.1 Arhinencephaly
Q04.2 Holoprosencephaly
Q04.3 Other reduction deformities of brain
Absence of part of brain
Agenesis of part of brain
Agyria
Aplasia of part of brain
Hydranencephaly
Hypoplasia of part of brain
Lissencephaly
Microgyria
Pachygyria
Excludes1 congenital malformations of corpus callosum (Q04.0)
Q04.4 Septo-optic dysplasia of brain
Q04.5 Megalencephaly
Q04.6 Congenital cerebral cysts
Porencephaly
Schizencephaly
Excludes1 acquired porencephalic cyst (G93.0)
Q04.8 Other specified congenital malformations of brain
Arnold-Chiari syndrome, type IV
Macrogyria
Q04.9 Congenital malformation of brain, unspecified
Congenital anomaly NOS of brain
Congenital deformity NOS of brain
Congenital disease or lesion NOS of brain
Multiple anomalies NOS of brain, congenital