ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 17  /  Q30-Q34  /  Q33
Q33 Congenital malformations of lung
Q33.0 Congenital cystic lung
Congenital cystic lung disease
Congenital honeycomb lung
Congenital polycystic lung disease
Excludes1 cystic fibrosis (E84.0)
cystic lung disease, acquired or unspecified (J98.4)
Q33.1 Accessory lobe of lung
Azygos lobe (fissured), lung
Q33.2 Sequestration of lung
Q33.3 Agenesis of lung
Congenital absence of lung (lobe)
Q33.4 Congenital bronchiectasis
Q33.5 Ectopic tissue in lung
Q33.6 Congenital hypoplasia and dysplasia of lung
Excludes1 pulmonary hypoplasia associated with short gestation (P28.0)
Q33.8 Other congenital malformations of lung
Q33.9 Congenital malformation of lung, unspecified