|  Q82 |  | Other congenital malformations of skin  | 
	
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		| Excludes1 | acrodermatitis enteropathica (E83.2) congenital erythropoietic porphyria (E80.0)
 pilonidal cyst or sinus (L05.-)
 Sturge-Weber (-Dimitri) syndrome (Q85.89)
 
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		|  Q82.0 |  | Hereditary lymphedema |  | 
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		|  Q82.1 |  | Xeroderma pigmentosum |  | 
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		|  Q82.2 |  | Congenital cutaneous mastocytosis |  
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| Congenital diffuse cutaneous mastocytosis |  | Congenital maculopapular cutaneous mastocytosis |  | Congenital urticaria pigmentosa |  
		| Excludes1 | cutaneous mastocytosis NOS (D47.01) diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
 malignant mastocytosis (C96.2-)
 systemic mastocytosis (D47.02)
 urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
 
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		|  Q82.3 |  | Incontinentia pigmenti |  | 
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		|  Q82.4 |  | Ectodermal dysplasia (anhidrotic) |  
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		| Excludes1 | Ellis-van Creveld syndrome (Q77.6) 
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		|  Q82.5 |  | Congenital non-neoplastic nevus |  
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| Birthmark NOS |  | Flammeus Nevus |  | Portwine Nevus |  | Sanguineous Nevus |  | Strawberry Nevus |  | Vascular Nevus NOS |  | Verrucous Nevus |  
		| Excludes2 | Café au lait spots (L81.3) lentigo (L81.4)
 nevus NOS (D22.-)
 araneus nevus (I78.1)
 melanocytic nevus (D22.-)
 pigmented nevus (D22.-)
 spider nevus (I78.1)
 stellar nevus (I78.1)
 
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		|  Q82.6 |  | Congenital sacral dimple |  
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| Parasacral dimple |  
		| Excludes2 | pilonidal cyst with abscess (L05.01) pilonidal cyst without abscess (L05.91)
 
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		|  Q82.8 |  | Other specified congenital malformations of skin |  
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| Abnormal palmar creases |  | Accessory skin tags |  | Benign familial pemphigus [Hailey-Hailey] |  | Congenital poikiloderma |  | Cutis laxa (hyperelastica) |  | Dermatoglyphic anomalies |  | Inherited keratosis palmaris et plantaris |  | Keratosis follicularis [Darier-White] |  
		| Excludes1 | Ehlers-Danlos syndromes (Q79.6-) 
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		| Excludes2 | disorders of pyrophosphate metabolism (E83.82-) 
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		|  Q82.9 |  | Congenital malformation of skin, unspecified |  |