ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 6  /  G10-G14

Systemic atrophies primarily affecting the central nervous system (G10-G14)

G10 Huntington's disease
Huntington's chorea
Huntington's dementia
UseAdditionalCode code, if applicable, to identify:
dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
mild neurocognitive disorder due to known physiological condition (F06.7-)
G11 Hereditary ataxia
Excludes2 cerebral palsy (G80.-)
hereditary and idiopathic neuropathy (G60.-)
metabolic disorders (E70-E88)
G11.0 Congenital nonprogressive ataxia
G11.1 Early-onset cerebellar ataxia
G11.10 Early-onset cerebellar ataxia, unspecified
G11.11 Friedreich ataxia
Autosomal recessive Friedreich ataxia
Friedreich ataxia with retained reflexes
G11.19 Other early-onset cerebellar ataxia
Early-onset cerebellar ataxia with essential tremor
Early-onset cerebellar ataxia with myoclonus [Hunt's ataxia]
Early-onset cerebellar ataxia with retained tendon reflexes
X-linked recessive spinocerebellar ataxia
G11.2 Late-onset cerebellar ataxia
age Adult: [15-124]
G11.3 Cerebellar ataxia with defective DNA repair
Ataxia telangiectasia [Louis-Bar]
Excludes2 Cockayne's syndrome (Q87.19)
other disorders of purine and pyrimidine metabolism (E79.-)
xeroderma pigmentosum (Q82.1)
G11.4 Hereditary spastic paraplegia
G11.5 Hypomyelination - hypogonadotropic hypogonadism - hypodontia
4H syndrome
Pol III-related leukodystrophy
G11.6 Leukodystrophy with vanishing white matter disease
G11.8 Other hereditary ataxias
G11.9 Hereditary ataxia, unspecified
Hereditary cerebellar ataxia NOS
Hereditary cerebellar degeneration
Hereditary cerebellar disease
Hereditary cerebellar syndrome
G12 Spinal muscular atrophy and related syndromes
G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
G12.1 Other inherited spinal muscular atrophy
Adult form spinal muscular atrophy
Childhood form, type II spinal muscular atrophy
Distal spinal muscular atrophy
Juvenile form, type III spinal muscular atrophy [Kugelberg-Welander]
Progressive bulbar palsy of childhood [Fazio-Londe]
Scapuloperoneal form spinal muscular atrophy
G12.2 Motor neuron disease
G12.20 Motor neuron disease, unspecified
G12.21 Amyotrophic lateral sclerosis
age Adult: [15-124]
G12.22 Progressive bulbar palsy
G12.23 Primary lateral sclerosis
G12.24 Familial motor neuron disease
G12.25 Progressive spinal muscle atrophy
G12.29 Other motor neuron disease
G12.8 Other spinal muscular atrophies and related syndromes
G12.9 Spinal muscular atrophy, unspecified
G13 Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere
G13.0 Paraneoplastic neuromyopathy and neuropathy
Carcinomatous neuromyopathy
Sensorial paraneoplastic neuropathy [Denny Brown]
CodeFirst underlying neoplasm (C00-D49)
nonPrimary Yes
G13.1 Other systemic atrophy primarily affecting central nervous system in neoplastic disease
Paraneoplastic limbic encephalopathy
CodeFirst underlying neoplasm (C00-D49)
nonPrimary Yes
G13.2 Systemic atrophy primarily affecting the central nervous system in myxedema
CodeFirst underlying disease, such as:
hypothyroidism (E03.-)
myxedematous congenital iodine deficiency (E00.1)
nonPrimary Yes
G13.8 Systemic atrophy primarily affecting central nervous system in other diseases classified elsewhere
CodeFirst underlying disease
nonPrimary Yes
G14 Postpolio syndrome
Includes postpolio myelitic syndrome
Excludes1 sequelae of poliomyelitis (B91)