ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 10  /  J80-J84

Other respiratory diseases principally affecting the interstitium (J80-J84)

J80 Acute respiratory distress syndrome
Acute respiratory distress syndrome in adult or child
Adult hyaline membrane disease
Excludes1 respiratory distress syndrome in newborn (perinatal) (P22.0)
J81 Pulmonary edema
UseAdditionalCode code to identify:
exposure to environmental tobacco smoke (Z77.22)
history of tobacco dependence (Z87.891)
occupational exposure to environmental tobacco smoke (Z57.31)
tobacco dependence (F17.-)
tobacco use (Z72.0)
Excludes1 chemical (acute) pulmonary edema (J68.1)
hypostatic pneumonia (J18.2)
passive pneumonia (J18.2)
pulmonary edema due to external agents (J60-J70)
pulmonary edema with heart disease NOS (I50.1)
pulmonary edema with heart failure (I50.1)
J81.0 Acute pulmonary edema
Acute edema of lung
J81.1 Chronic pulmonary edema
Pulmonary congestion (chronic) (passive)
Pulmonary edema NOS
J82 Pulmonary eosinophilia, not elsewhere classified
Excludes2 pulmonary eosinophilia due to aspergillosis (B44.-)
pulmonary eosinophilia due to drugs (J70.2-J70.4)
pulmonary eosinophilia due to specified parasitic infection (B50-B83)
pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)
pulmonary infiltrate NOS (R91.8)
J82.8 Pulmonary eosinophilia, not elsewhere classified
J82.81 Chronic eosinophilic pneumonia
Eosinophilic pneumonia, NOS
J82.82 Acute eosinophilic pneumonia
J82.83 Eosinophilic asthma
CodeFirst asthma, by type, such as:
mild intermittent asthma (J45.2-)
mild persistent asthma (J45.3-)
moderate persistent asthma (J45.4-)
severe persistent asthma (J45.5-)
J82.89 Other pulmonary eosinophilia, not elsewhere classified
Allergic pneumonia
Löffler's pneumonia
Tropical (pulmonary) eosinophilia NOS
J84 Other interstitial pulmonary diseases
Excludes1 drug-induced interstitial lung disorders (J70.2-J70.4)
interstitial emphysema (J98.2)
Excludes2 lung diseases due to external agents (J60-J70)
J84.0 Alveolar and parieto-alveolar conditions
J84.01 Alveolar proteinosis
J84.02 Pulmonary alveolar microlithiasis
J84.03 Idiopathic pulmonary hemosiderosis
Essential brown induration of lung
CodeFirst underlying disease, such as:
disorders of iron metabolism (E83.1-)
Excludes1 acute idiopathic pulmonary hemorrhage in infants [AIPHI] (R04.81)
nonPrimary Yes
J84.09 Other alveolar and parieto-alveolar conditions
J84.1 Other interstitial pulmonary diseases with fibrosis
Excludes1 pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
pulmonary fibrosis (chronic) following radiation (J70.1)
J84.10 Pulmonary fibrosis, unspecified
Capillary fibrosis of lung
Cirrhosis of lung (chronic) NOS
Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS
Induration of lung (chronic) NOS
Postinflammatory pulmonary fibrosis
J84.11 Idiopathic interstitial pneumonia
Excludes1 lymphoid interstitial pneumonia (J84.2)
pneumocystis pneumonia (B59)
J84.111 Idiopathic interstitial pneumonia, not otherwise specified
J84.112 Idiopathic pulmonary fibrosis
Cryptogenic fibrosing alveolitis
Idiopathic fibrosing alveolitis
J84.113 Idiopathic non-specific interstitial pneumonitis
Excludes1 non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89)
J84.114 Acute interstitial pneumonitis
Hamman-Rich syndrome
Excludes1 pneumocystis pneumonia (B59)
J84.115 Respiratory bronchiolitis interstitial lung disease
J84.116 Cryptogenic organizing pneumonia
Excludes1 organizing pneumonia NOS, or due to known underlying cause (J84.89)
J84.117 Desquamative interstitial pneumonia
J84.17 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
nonPrimary Yes
J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
Progressive fibrotic interstitial lung disease
CodeFirst underlying disease, such as:
lung diseases due to external agents (J60-J70)
rheumatoid arthritis (M05.00-M06.9)
sarcoidosis (D86.-)
systemic connective tissue disorders (M30-M36)
J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
Organizing pneumonia due to collagen vascular disease
Organizing pneumonia in diseases classified elsewhere
CodeFirst underlying disease, such as:
progressive systemic sclerosis (M34.0)
rheumatoid arthritis (M05.00-M06.9)
systemic lupus erythematosis (M32.0-M32.9)
J84.2 Lymphoid interstitial pneumonia
Lymphoid interstitial pneumonitis
J84.8 Other specified interstitial pulmonary diseases
Excludes1 exogenous lipoid pneumonia (J69.1)
unspecified lipoid pneumonia (J69.1)
J84.81 Lymphangioleiomyomatosis
Lymphangiomyomatosis
J84.82 Adult pulmonary Langerhans cell histiocytosis
Adult PLCH
age Adult: [15-124]
J84.83 Surfactant mutations of the lung
J84.84 Other interstitial lung diseases of childhood
J84.841 Neuroendocrine cell hyperplasia of infancy
J84.842 Pulmonary interstitial glycogenosis
J84.843 Alveolar capillary dysplasia with vein misalignment
J84.848 Other interstitial lung diseases of childhood
J84.89 Other specified interstitial pulmonary diseases
Endogenous lipoid pneumonia
Interstitial pneumonitis
Non-specific interstitial pneumonitis NOS
Organizing pneumonia NOS
CodeFirst , if applicable:
poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
underlying cause of pneumonopathy, if known
UseAdditionalCode code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced
Excludes1 cryptogenic organizing pneumonia (J84.116)
idiopathic non-specific interstitial pneumonitis (J84.113)
lipoid pneumonia, exogenous or unspecified (J69.1)
lymphoid interstitial pneumonia (J84.2)
J84.9 Interstitial pulmonary disease, unspecified
Interstitial pneumonia NOS