ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 13  /  M04

Autoinflammatory syndromes (M04)

M04 Autoinflammatory syndromes
Excludes2 Crohn's disease (K50.-)
M04.1 Periodic fever syndromes
Familial Mediterranean fever
Hyperimmunoglobin D syndrome
Mevalonate kinase deficiency
Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
M04.2 Cryopyrin-associated periodic syndromes
Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
Familial cold autoinflammatory syndrome
Familial cold urticaria
Muckle-Wells syndrome
Neonatal onset multisystemic inflammatory disorder [NOMID]
M04.8 Other autoinflammatory syndromes
Blau syndrome
Deficiency of interleukin 1 receptor antagonist [DIRA]
Majeed syndrome
Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]
M04.9 Autoinflammatory syndrome, unspecified