ICD-10-CM Book 2026 Edition

Chapters  /  Chapter 17  /  Q10-Q18

Congenital malformations of eye, ear, face and neck (Q10-Q18)

Excludes2: cleft lip and cleft palate (Q35-Q37)
congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)
congenital malformation of larynx (Q31.-)
congenital malformation of lip NEC (Q38.0)
congenital malformation of nose (Q30.-)
congenital malformation of parathyroid gland (Q89.2)
congenital malformation of thyroid gland (Q89.2)
Q10 Congenital malformations of eyelid, lacrimal apparatus and orbit
Excludes1 cryptophthalmos NOS (Q11.2)
cryptophthalmos syndrome (Q87.0)
Q10.0 Congenital ptosis
Q10.1 Congenital ectropion
Q10.2 Congenital entropion
Q10.3 Other congenital malformations of eyelid
Ablepharon
Blepharophimosis, congenital
Coloboma of eyelid
Congenital absence or agenesis of cilia
Congenital absence or agenesis of eyelid
Congenital accessory eyelid
Congenital accessory eye muscle
Congenital malformation of eyelid NOS
Q10.4 Absence and agenesis of lacrimal apparatus
Congenital absence of punctum lacrimale
Q10.5 Congenital stenosis and stricture of lacrimal duct
Q10.6 Other congenital malformations of lacrimal apparatus
Congenital malformation of lacrimal apparatus NOS
Q10.7 Congenital malformation of orbit
Q11 Anophthalmos, microphthalmos and macrophthalmos
Q11.0 Cystic eyeball
Q11.1 Other anophthalmos
Anophthalmos NOS
Agenesis of eye
Aplasia of eye
Q11.2 Microphthalmos
Cryptophthalmos NOS
Dysplasia of eye
Hypoplasia of eye
Rudimentary eye
Excludes1 cryptophthalmos syndrome (Q87.0)
Q11.3 Macrophthalmos
Excludes1 macrophthalmos in congenital glaucoma (Q15.0)
Q12 Congenital lens malformations
Q12.0 Congenital cataract
Q12.1 Congenital displaced lens
Q12.2 Coloboma of lens
Q12.3 Congenital aphakia
Q12.4 Spherophakia
Q12.8 Other congenital lens malformations
Microphakia
Q12.9 Congenital lens malformation, unspecified
Q13 Congenital malformations of anterior segment of eye
Q13.0 Coloboma of iris
Coloboma NOS
Q13.1 Absence of iris
Aniridia
UseAdditionalCode code for associated glaucoma (H42)
Q13.2 Other congenital malformations of iris
Anisocoria, congenital
Atresia of pupil
Congenital malformation of iris NOS
Corectopia
Q13.3 Congenital corneal opacity
Q13.4 Other congenital corneal malformations
Congenital malformation of cornea NOS
Microcornea
Peter's anomaly
Q13.5 Blue sclera
Q13.8 Other congenital malformations of anterior segment of eye
Q13.81 Rieger anomaly
Axenfeld-Rieger syndrome
CodeAlso any other associated congenital malformations such as cardiac defects
UseAdditionalCode code for associated glaucoma (H42)
Q13.89 Other congenital malformations of anterior segment of eye
Q13.9 Congenital malformation of anterior segment of eye, unspecified
Q14 Congenital malformations of posterior segment of eye
Excludes2 optic nerve hypoplasia (H47.03-)
Q14.0 Congenital malformation of vitreous humor
Congenital vitreous opacity
Q14.1 Congenital malformation of retina
Congenital retinal aneurysm
Q14.2 Congenital malformation of optic disc
Coloboma of optic disc
Q14.3 Congenital malformation of choroid
Q14.8 Other congenital malformations of posterior segment of eye
Coloboma of the fundus
Q14.9 Congenital malformation of posterior segment of eye, unspecified
Q15 Other congenital malformations of eye
Excludes1 congenital nystagmus (H55.01)
ocular albinism (E70.31-)
optic nerve hypoplasia (H47.03-)
retinitis pigmentosa (H35.52)
Q15.0 Congenital glaucoma
Axenfeld's anomaly
Buphthalmos
Glaucoma of childhood
Glaucoma of newborn
Hydrophthalmos
Keratoglobus, congenital, with glaucoma
Macrocornea with glaucoma
Macrophthalmos in congenital glaucoma
Megalocornea with glaucoma
Q15.8 Other specified congenital malformations of eye
Q15.9 Congenital malformation of eye, unspecified
Congenital anomaly of eye
Congenital deformity of eye
Q16 Congenital malformations of ear causing impairment of hearing
Excludes1 congenital deafness (H90.-)
Q16.0 Congenital absence of (ear) auricle
Q16.1 Congenital absence, atresia and stricture of auditory canal (external)
Congenital atresia or stricture of osseous meatus
Q16.2 Absence of eustachian tube
Q16.3 Congenital malformation of ear ossicles
Congenital fusion of ear ossicles
Q16.4 Other congenital malformations of middle ear
Congenital malformation of middle ear NOS
Q16.5 Congenital malformation of inner ear
Congenital anomaly of membranous labyrinth
Congenital anomaly of organ of Corti
Q16.9 Congenital malformation of ear causing impairment of hearing, unspecified
Congenital absence of ear NOS
Q17 Other congenital malformations of ear
Excludes1 congenital malformations of ear with impairment of hearing (Q16.0-Q16.9)
preauricular sinus (Q18.1)
Q17.0 Accessory auricle
Accessory tragus
Polyotia
Preauricular appendage or tag
Supernumerary ear
Supernumerary lobule
Q17.1 Macrotia
Q17.2 Microtia
Q17.3 Other misshapen ear
Pointed ear
Q17.4 Misplaced ear
Low-set ears
Excludes1 cervical auricle (Q18.2)
Q17.5 Prominent ear
Bat ear
Q17.8 Other specified congenital malformations of ear
Congenital absence of lobe of ear
Q17.9 Congenital malformation of ear, unspecified
Congenital anomaly of ear NOS
Q18 Other congenital malformations of face and neck
Excludes1 cleft lip and cleft palate (Q35-Q37)
conditions classified to Q67.0-Q67.4
congenital malformations of skull and face bones (Q75.-)
cyclopia (Q87.0)
dentofacial anomalies [including malocclusion] (M26.-)
malformation syndromes affecting facial appearance (Q87.0)
persistent thyroglossal duct (Q89.2)
Q18.0 Sinus, fistula and cyst of branchial cleft
Branchial vestige
Q18.1 Preauricular sinus and cyst
Fistula of auricle, congenital
Cervicoaural fistula
Q18.2 Other branchial cleft malformations
Branchial cleft malformation NOS
Cervical auricle
Otocephaly
Q18.3 Webbing of neck
Pterygium colli
Q18.4 Macrostomia
Q18.5 Microstomia
Q18.6 Macrocheilia
Hypertrophy of lip, congenital
Q18.7 Microcheilia
Q18.8 Other specified congenital malformations of face and neck
Medial cyst of face and neck
Medial fistula of face and neck
Medial sinus of face and neck
Q18.9 Congenital malformation of face and neck, unspecified
Congenital anomaly NOS of face and neck