ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 17  /  Q38-Q45

Other congenital malformations of the digestive system (Q38-Q45)

Q38 Other congenital malformations of tongue, mouth and pharynx
Excludes1 dentofacial anomalies (M26.-)
macrostomia (Q18.4)
microstomia (Q18.5)
Q38.0 Congenital malformations of lips, not elsewhere classified
Congenital fistula of lip
Congenital malformation of lip NOS
Van der Woude's syndrome
Excludes1 cleft lip (Q36.-)
cleft lip with cleft palate (Q37.-)
macrocheilia (Q18.6)
microcheilia (Q18.7)
Q38.1 Ankyloglossia
Tongue tie
Q38.2 Macroglossia
Congenital hypertrophy of tongue
Q38.3 Other congenital malformations of tongue
Aglossia
Bifid tongue
Congenital adhesion of tongue
Congenital fissure of tongue
Congenital malformation of tongue NOS
Double tongue
Hypoglossia
Hypoplasia of tongue
Microglossia
Q38.4 Congenital malformations of salivary glands and ducts
Atresia of salivary glands and ducts
Congenital absence of salivary glands and ducts
Congenital accessory salivary glands and ducts
Congenital fistula of salivary gland
Q38.5 Congenital malformations of palate, not elsewhere classified
Congenital absence of uvula
Congenital malformation of palate NOS
Congenital high arched palate
Excludes1 cleft palate (Q35.-)
cleft palate with cleft lip (Q37.-)
Q38.6 Other congenital malformations of mouth
Congenital malformation of mouth NOS
Q38.7 Congenital pharyngeal pouch
Congenital diverticulum of pharynx
Excludes1 pharyngeal pouch syndrome (D82.1)
Q38.8 Other congenital malformations of pharynx
Congenital malformation of pharynx NOS
Imperforate pharynx
Q39 Congenital malformations of esophagus
Q39.0 Atresia of esophagus without fistula
Atresia of esophagus NOS
Q39.1 Atresia of esophagus with tracheo-esophageal fistula
Atresia of esophagus with broncho-esophageal fistula
Q39.2 Congenital tracheo-esophageal fistula without atresia
Congenital tracheo-esophageal fistula NOS
Q39.3 Congenital stenosis and stricture of esophagus
Q39.4 Esophageal web
Q39.5 Congenital dilatation of esophagus
Congenital cardiospasm
Q39.6 Congenital diverticulum of esophagus
Congenital esophageal pouch
Q39.8 Other congenital malformations of esophagus
Congenital absence of esophagus
Congenital displacement of esophagus
Congenital duplication of esophagus
Q39.9 Congenital malformation of esophagus, unspecified
Q40 Other congenital malformations of upper alimentary tract
Q40.0 Congenital hypertrophic pyloric stenosis
Congenital or infantile constriction
Congenital or infantile hypertrophy
Congenital or infantile spasm
Congenital or infantile stenosis
Congenital or infantile stricture
Q40.1 Congenital hiatus hernia
Congenital displacement of cardia through esophageal hiatus
Excludes1 congenital diaphragmatic hernia (Q79.0)
Q40.2 Other specified congenital malformations of stomach
Congenital displacement of stomach
Congenital diverticulum of stomach
Congenital hourglass stomach
Congenital duplication of stomach
Megalogastria
Microgastria
Q40.3 Congenital malformation of stomach, unspecified
Q40.8 Other specified congenital malformations of upper alimentary tract
Q40.9 Congenital malformation of upper alimentary tract, unspecified
Congenital anomaly of upper alimentary tract
Congenital deformity of upper alimentary tract
Q41 Congenital absence, atresia and stenosis of small intestine
Includes congenital obstruction, occlusion or stricture of small intestine or intestine NOS
Excludes1 cystic fibrosis with intestinal manifestation (E84.11)
meconium ileus NOS (without cystic fibrosis) (P76.0)
Q41.0 Congenital absence, atresia and stenosis of duodenum
Q41.1 Congenital absence, atresia and stenosis of jejunum
Apple peel syndrome
Imperforate jejunum
Q41.2 Congenital absence, atresia and stenosis of ileum
Q41.8 Congenital absence, atresia and stenosis of other specified parts of small intestine
Q41.9 Congenital absence, atresia and stenosis of small intestine, part unspecified
Congenital absence, atresia and stenosis of intestine NOS
Q42 Congenital absence, atresia and stenosis of large intestine
Includes congenital obstruction, occlusion and stricture of large intestine
Q42.0 Congenital absence, atresia and stenosis of rectum with fistula
Q42.1 Congenital absence, atresia and stenosis of rectum without fistula
Imperforate rectum
Q42.2 Congenital absence, atresia and stenosis of anus with fistula
Q42.3 Congenital absence, atresia and stenosis of anus without fistula
Imperforate anus
Q42.8 Congenital absence, atresia and stenosis of other parts of large intestine
Q42.9 Congenital absence, atresia and stenosis of large intestine, part unspecified
Q43 Other congenital malformations of intestine
Q43.0 Meckel's diverticulum (displaced) (hypertrophic)
Persistent omphalomesenteric duct
Persistent vitelline duct
Q43.1 Hirschsprung's disease
Aganglionosis
Congenital (aganglionic) megacolon
Q43.2 Other congenital functional disorders of colon
Congenital dilatation of colon
Q43.3 Congenital malformations of intestinal fixation
Congenital omental, anomalous adhesions [bands]
Congenital peritoneal adhesions [bands]
Incomplete rotation of cecum and colon
Insufficient rotation of cecum and colon
Jackson's membrane
Malrotation of colon
Rotation failure of cecum and colon
Universal mesentery
Q43.4 Duplication of intestine
Q43.5 Ectopic anus
Q43.6 Congenital fistula of rectum and anus
Excludes1 congenital fistula of anus with absence, atresia and stenosis (Q42.2)
congenital fistula of rectum with absence, atresia and stenosis (Q42.0)
congenital rectovaginal fistula (Q52.2)
congenital urethrorectal fistula (Q64.73)
pilonidal fistula or sinus (L05.-)
Q43.7 Persistent cloaca
Cloaca NOS
Q43.8 Other specified congenital malformations of intestine
Congenital blind loop syndrome
Congenital diverticulitis, colon
Congenital diverticulum, intestine
Dolichocolon
Megaloappendix
Megaloduodenum
Microcolon
Transposition of appendix
Transposition of colon
Transposition of intestine
Q43.9 Congenital malformation of intestine, unspecified
Q44 Congenital malformations of gallbladder, bile ducts and liver
Q44.0 Agenesis, aplasia and hypoplasia of gallbladder
Congenital absence of gallbladder
Q44.1 Other congenital malformations of gallbladder
Congenital malformation of gallbladder NOS
Intrahepatic gallbladder
Q44.2 Atresia of bile ducts
Q44.3 Congenital stenosis and stricture of bile ducts
Q44.4 Choledochal cyst
Q44.5 Other congenital malformations of bile ducts
Accessory hepatic duct
Biliary duct duplication
Congenital malformation of bile duct NOS
Cystic duct duplication
Q44.6 Cystic disease of liver
Fibrocystic disease of liver
Q44.7 Other congenital malformations of liver
CodeAlso , if applicable, associated malformations affecting other systems
Q44.70 Other congenital malformation of liver, unspecified
Congenital malformation of liver, NOS
Q44.71 Alagille syndrome
Alagille-Watson syndrome
Q44.79 Other congenital malformations of liver
Accessory liver
Congenital absence of liver
Congenital hepatomegaly
Q45 Other congenital malformations of digestive system
Excludes2 congenital diaphragmatic hernia (Q79.0)
congenital hiatus hernia (Q40.1)
Q45.0 Agenesis, aplasia and hypoplasia of pancreas
Congenital absence of pancreas
Q45.1 Annular pancreas
Q45.2 Congenital pancreatic cyst
Q45.3 Other congenital malformations of pancreas and pancreatic duct
Accessory pancreas
Congenital malformation of pancreas or pancreatic duct NOS
Excludes1 congenital diabetes mellitus (E10.-)
cystic fibrosis (E84.0-E84.9)
fibrocystic disease of pancreas (E84.-)
neonatal diabetes mellitus (P70.2)
Q45.8 Other specified congenital malformations of digestive system
Absence (complete) (partial) of alimentary tract NOS
Duplication of digestive system
Malposition, congenital of digestive system
Q45.9 Congenital malformation of digestive system, unspecified
Congenital anomaly of digestive system
Congenital deformity of digestive system