ICD-10-CM Book 2026 Edition

Chapters  /  Chapter 17  /  Q60-Q64

Congenital malformations of the urinary system (Q60-Q64)

Q60 Renal agenesis and other reduction defects of kidney
Includes congenital absence of kidney
congenital atrophy of kidney
infantile atrophy of kidney
Q60.0 Renal agenesis, unilateral
Q60.1 Renal agenesis, bilateral
Q60.2 Renal agenesis, unspecified
Q60.3 Renal hypoplasia, unilateral
Q60.4 Renal hypoplasia, bilateral
Q60.5 Renal hypoplasia, unspecified
Q60.6 Potter's syndrome
Q61 Cystic kidney disease
Excludes1 acquired cyst of kidney (N28.1)
Potter's syndrome (Q60.6)
Q61.0 Congenital renal cyst
Q61.00 Congenital renal cyst, unspecified
Cyst of kidney NOS (congenital)
Q61.01 Congenital single renal cyst
Q61.02 Congenital multiple renal cysts
Q61.1 Polycystic kidney, infantile type
Polycystic kidney, autosomal recessive
Q61.11 Cystic dilatation of collecting ducts
Q61.19 Other polycystic kidney, infantile type
Q61.2 Polycystic kidney, adult type
Polycystic kidney, autosomal dominant
Q61.3 Polycystic kidney, unspecified
Q61.4 Renal dysplasia
Multicystic dysplastic kidney
Multicystic kidney (development)
Multicystic kidney disease
Multicystic renal dysplasia
Excludes1 polycystic kidney disease (Q61.11-Q61.3)
Q61.5 Medullary cystic kidney
Nephronophthisis
Sponge kidney NOS
Q61.8 Other cystic kidney diseases
Fibrocystic kidney
Fibrocystic renal degeneration or disease
Q61.9 Cystic kidney disease, unspecified
Meckel-Gruber syndrome
Q62 Congenital obstructive defects of renal pelvis and congenital malformations of ureter
Q62.0 Congenital hydronephrosis
Q62.1 Congenital occlusion of ureter
Atresia and stenosis of ureter
Q62.10 Congenital occlusion of ureter, unspecified
Q62.11 Congenital occlusion of ureteropelvic junction
Q62.12 Congenital occlusion of ureterovesical orifice
Q62.2 Congenital megaureter
Congenital dilatation of ureter
Q62.3 Other obstructive defects of renal pelvis and ureter
Q62.31 Congenital ureterocele, orthotopic
Q62.32 Cecoureterocele
Ectopic ureterocele
Q62.39 Other obstructive defects of renal pelvis and ureter
Ureteropelvic junction obstruction NOS
Q62.4 Agenesis of ureter
Congenital absence ureter
Q62.5 Duplication of ureter
Accessory ureter
Double ureter
Q62.6 Malposition of ureter
Q62.60 Malposition of ureter, unspecified
Q62.61 Deviation of ureter
Q62.62 Displacement of ureter
Q62.63 Anomalous implantation of ureter
Ectopia of ureter
Ectopic ureter
Q62.69 Other malposition of ureter
Q62.7 Congenital vesico-uretero-renal reflux
Q62.8 Other congenital malformations of ureter
Anomaly of ureter NOS
Q63 Other congenital malformations of kidney
Excludes1 congenital nephrotic syndrome (N04.-)
Q63.0 Accessory kidney
Q63.1 Lobulated, fused and horseshoe kidney
Q63.2 Ectopic kidney
Congenital displaced kidney
Malrotation of kidney
Q63.3 Hyperplastic and giant kidney
Compensatory hypertrophy of kidney
Q63.8 Other specified congenital malformations of kidney
Congenital renal calculi
Q63.9 Congenital malformation of kidney, unspecified
Q64 Other congenital malformations of urinary system
Q64.0 Epispadias
Excludes1 hypospadias (Q54.-)
Q64.1 Exstrophy of urinary bladder
Q64.10 Exstrophy of urinary bladder, unspecified
Ectopia vesicae
Q64.11 Supravesical fissure of urinary bladder
Q64.12 Cloacal exstrophy of urinary bladder
Q64.19 Other exstrophy of urinary bladder
Extroversion of bladder
Q64.2 Congenital posterior urethral valves
Q64.3 Other atresia and stenosis of urethra and bladder neck
Q64.31 Congenital bladder neck obstruction
Congenital obstruction of vesicourethral orifice
Q64.32 Congenital stricture of urethra
Q64.33 Congenital stricture of urinary meatus
Q64.39 Other atresia and stenosis of urethra and bladder neck
Atresia and stenosis of urethra and bladder neck NOS
Q64.4 Malformation of urachus
Cyst of urachus
Patent urachus
Prolapse of urachus
Q64.5 Congenital absence of bladder and urethra
Q64.6 Congenital diverticulum of bladder
Q64.7 Other and unspecified congenital malformations of bladder and urethra
Excludes1 congenital prolapse of bladder (mucosa) (Q79.4)
Q64.70 Unspecified congenital malformation of bladder and urethra
Malformation of bladder or urethra NOS
Q64.71 Congenital prolapse of urethra
Q64.72 Congenital prolapse of urinary meatus
Q64.73 Congenital urethrorectal fistula
Q64.74 Double urethra
Q64.75 Double urinary meatus
Q64.79 Other congenital malformations of bladder and urethra
Q64.8 Other specified congenital malformations of urinary system
Q64.9 Congenital malformation of urinary system, unspecified
Congenital anomaly NOS of urinary system
Congenital deformity NOS of urinary system