ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 3  /  D55-D59  /  D56
D56 Thalassemia
Excludes1 sickle-cell thalassemia (D57.4-)
D56.0 Alpha thalassemia
Alpha thalassemia major
Hemoglobin H Constant Spring
Hemoglobin H disease
Hydrops fetalis due to alpha thalassemia
Severe alpha thalassemia
Triple gene defect alpha thalassemia
UseAdditionalCode code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
Excludes1 alpha thalassemia trait or minor (D56.3)
asymptomatic alpha thalassemia (D56.3)
hydrops fetalis due to isoimmunization (P56.0)
hydrops fetalis not due to immune hemolysis (P83.2)
D56.1 Beta thalassemia
Beta thalassemia major
Cooley's anemia
Homozygous beta thalassemia
Severe beta thalassemia
Thalassemia intermedia
Thalassemia major
Excludes1 beta thalassemia minor (D56.3)
beta thalassemia trait (D56.3)
delta-beta thalassemia (D56.2)
hemoglobin E-beta thalassemia (D56.5)
sickle-cell beta thalassemia (D57.4-)
D56.2 Delta-beta thalassemia
Homozygous delta-beta thalassemia
Excludes1 delta-beta thalassemia minor (D56.3)
delta-beta thalassemia trait (D56.3)
D56.3 Thalassemia minor
Alpha thalassemia minor
Alpha thalassemia silent carrier
Alpha thalassemia trait
Beta thalassemia minor
Beta thalassemia trait
Delta-beta thalassemia minor
Delta-beta thalassemia trait
Thalassemia trait NOS
Excludes1 alpha thalassemia (D56.0)
beta thalassemia (D56.1)
delta-beta thalassemia (D56.2)
hemoglobin E-beta thalassemia (D56.5)
sickle-cell trait (D57.3)
D56.4 Hereditary persistence of fetal hemoglobin [HPFH]
D56.5 Hemoglobin E-beta thalassemia
Excludes1 beta thalassemia (D56.1)
beta thalassemia minor (D56.3)
beta thalassemia trait (D56.3)
delta-beta thalassemia (D56.2)
delta-beta thalassemia trait (D56.3)
hemoglobin E disease (D58.2)
other hemoglobinopathies (D58.2)
sickle-cell beta thalassemia (D57.4-)
D56.8 Other thalassemias
Dominant thalassemia
Hemoglobin C thalassemia
Mixed thalassemia
Thalassemia with other hemoglobinopathy
Excludes1 hemoglobin C disease (D58.2)
hemoglobin E disease (D58.2)
other hemoglobinopathies (D58.2)
sickle-cell anemia (D57.-)
sickle-cell thalassemia (D57.4-)
D56.9 Thalassemia, unspecified
Mediterranean anemia (with other hemoglobinopathy)