D56 | 
		  | 
		Thalassemia  | 
	
	
		 |  | 
		
	
		| Excludes1 | 
		sickle-cell thalassemia (D57.4-)
  | 
	 
 
 | 
	
 |  | 
	
		 D56.0 | 
		  | 
		Alpha thalassemia | 
	 
	
		 |  | 
		
| Alpha thalassemia major |  | Hemoglobin H Constant Spring |  | Hemoglobin H disease |  | Hydrops fetalis due to alpha thalassemia |  | Severe alpha thalassemia |  | Triple gene defect alpha thalassemia |  	
		| UseAdditionalCode | 
		code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)
  | 
	 
	
		| Excludes1 | 
		alpha thalassemia trait or minor (D56.3) asymptomatic alpha thalassemia (D56.3) hydrops fetalis due to isoimmunization (P56.0) hydrops fetalis not due to immune hemolysis (P83.2)
  | 
	 
 
 | 
	   | 
 |  | 
	
		 D56.1 | 
		  | 
		Beta thalassemia | 
	 
	
		 |  | 
		
| Beta thalassemia major |  | Cooley's anemia |  | Homozygous beta thalassemia |  | Severe beta thalassemia |  | Thalassemia intermedia |  | Thalassemia major |  	
		| Excludes1 | 
		beta thalassemia minor (D56.3) beta thalassemia trait (D56.3) delta-beta thalassemia (D56.2) hemoglobin E-beta thalassemia (D56.5) sickle-cell beta thalassemia (D57.4-)
  | 
	 
 
 | 
	   | 
 |  | 
	
		 D56.2 | 
		  | 
		Delta-beta thalassemia | 
	 
	
		 |  | 
		
| Homozygous delta-beta thalassemia |  	
		| Excludes1 | 
		delta-beta thalassemia minor (D56.3) delta-beta thalassemia trait (D56.3)
  | 
	 
 
 | 
	   | 
 |  | 
	
		 D56.3 | 
		  | 
		Thalassemia minor | 
	 
	
		 |  | 
		
| Alpha thalassemia minor |  | Alpha thalassemia silent carrier |  | Alpha thalassemia trait |  | Beta thalassemia minor |  | Beta thalassemia trait |  | Delta-beta thalassemia minor |  | Delta-beta thalassemia trait |  | Thalassemia trait NOS |  	
		| Excludes1 | 
		alpha thalassemia (D56.0) beta thalassemia (D56.1) delta-beta thalassemia (D56.2) hemoglobin E-beta thalassemia (D56.5) sickle-cell trait (D57.3)
  | 
	 
 
 | 
	   | 
 |  | 
	
		 D56.4 | 
		 | 
		Hereditary persistence of fetal hemoglobin [HPFH] | 
	 
  | 
 |  | 
	
		 D56.5 | 
		  | 
		Hemoglobin E-beta thalassemia | 
	 
	
		 |  | 
		
	
		| Excludes1 | 
		beta thalassemia (D56.1) beta thalassemia minor (D56.3) beta thalassemia trait (D56.3) delta-beta thalassemia (D56.2) delta-beta thalassemia trait (D56.3) hemoglobin E disease (D58.2) other hemoglobinopathies (D58.2) sickle-cell beta thalassemia (D57.4-)
  | 
	 
 
 | 
	   | 
 |  | 
	
		 D56.8 | 
		  | 
		Other thalassemias | 
	 
	
		 |  | 
		
| Dominant thalassemia |  | Hemoglobin C thalassemia |  | Mixed thalassemia |  | Thalassemia with other hemoglobinopathy |  	
		| Excludes1 | 
		hemoglobin C disease (D58.2) hemoglobin E disease (D58.2) other hemoglobinopathies (D58.2) sickle-cell anemia (D57.-) sickle-cell thalassemia (D57.4-)
  | 
	 
 
 | 
	   | 
 |  | 
	
		 D56.9 | 
		  | 
		Thalassemia, unspecified | 
	 
	
		 |  | 
		
| Mediterranean anemia (with other hemoglobinopathy) |   
 | 
	   |