 E88 |
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Other and unspecified metabolic disorders  |
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| UseAdditionalCode |
codes for associated conditions
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| Excludes1 |
histiocytosis X (chronic) (C96.6)
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| E88.0 |
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Disorders of plasma-protein metabolism, not elsewhere classified |
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| Excludes1 |
monoclonal gammopathy (of undetermined significance) (D47.2)
polyclonal hypergammaglobulinemia (D89.0)
Waldenström macroglobulinemia (C88.00)
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| Excludes2 |
disorder of lipoprotein metabolism (E78.-)
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 E88.01 |
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Alpha-1-antitrypsin deficiency |
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| E88.02 |
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Plasminogen deficiency |
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| Dysplasminogenemia | | Hypoplasminogenemia | | Type 1 plasminogen deficiency | | Type 2 plasminogen deficiency |
| CodeAlso |
, if applicable, ligneous conjunctivitis (H10.51-)
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| UseAdditionalCode |
code for associated findings, such as:
hydrocephalus (G91.4)
otitis media (H67.-)
respiratory disorder related to plasminogen deficiency (J99)
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| E88.09 |
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Other disorders of plasma-protein metabolism, not elsewhere classified |
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| E88.1 |
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Lipodystrophy, not elsewhere classified |
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| Excludes1 |
Whipple's disease (K90.81)
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| E88.10 |
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Lipodystrophy, unspecified |
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| E88.11 |
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Partial lipodystrophy |
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| Acquired partial lipodystrophy (APL) | | Barraquer-Simons lipodystrophy | | Familial partial lipodystrophy (FPLD) |
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| E88.12 |
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Generalized lipodystrophy |
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| Acquired generalized lipodystrophy (AGL) | | Berardinelli-Siep syndrome | | Congenital generalized lipodystrophy (CGL) | | Lawrence syndrome |
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| E88.13 |
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Localized lipodystrophy |
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| Injection lipodystrophy | | Insulin lipodystrophy |
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| E88.14 |
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HIV-associated lipodystrophy |
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| CodeFirst |
any human immunodeficiency virus [HIV] disease (B20)
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| UseAdditionalCode |
code for adverse effect, if applicable, to identify drug (T37.5X5-)
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| E88.19 |
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Other lipodystrophy, not elsewhere classified |
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| E88.2 |
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Lipomatosis, not elsewhere classified |
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| Lipomatosis NOS | | Lipomatosis (Check) dolorosa [Dercum] |
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| E88.3 |
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Tumor lysis syndrome |
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| Tumor lysis syndrome (spontaneous) | | Tumor lysis syndrome following antineoplastic drug chemotherapy |
| UseAdditionalCode |
code for adverse effect, if applicable, to identify drug (T45.1X5)
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| E88.4 |
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Mitochondrial metabolism disorders |
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| Excludes1 |
disorders of pyruvate metabolism (E74.4)
Kearns-Sayre syndrome (H49.81)
Leber's disease (H47.22)
Leigh's encephalopathy (G31.82)
Mitochondrial myopathy, NEC (G71.3)
Reye's syndrome (G93.7)
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| E88.40 |
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Mitochondrial metabolism disorder, unspecified |
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| E88.41 |
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MELAS syndrome |
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| Mitochondrial myopathy, encephalopathy, lactic acidosis and stroke-like episodes |
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| E88.42 |
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MERRF syndrome |
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| Myoclonic epilepsy associated with ragged-red fibers |
| CodeAlso |
progressive myoclonic epilepsy (G40.3-)
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| E88.43 |
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Disorders of mitochondrial tRNA synthetases |
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| ARS2-related mitochondrial disorders | | LBSL | | Leukoencephalopathy with brainstem - spinal cord involvement - lactate elevation | | Leukoencephalopathy with thalamus - brainstem involvement - high lactate | | LTBL | | Mitochondrial aminoacyl-tRNA synthetase disorders |
| CodeAlso |
, if applicable, associated condition such as:
leukoencephalopathy (G93.49)
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| E88.49 |
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Other mitochondrial metabolism disorders |
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| E88.8 |
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Other specified metabolic disorders |
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| E88.81 |
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Metabolic syndrome and other insulin resistance |
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| UseAdditionalCode |
codes for associated manifestations, such as:
obesity (E66.-)
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| E88.810 |
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Metabolic syndrome |
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| E88.811 |
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Insulin resistance syndrome, Type A |
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| E88.818 |
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Other insulin resistance |
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| Insulin resistance syndrome, Type B |
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| E88.819 |
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Insulin resistance, unspecified |
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| E88.82 |
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Obesity due to disruption of MC4R pathway |
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| UseAdditionalCode |
code, if applicable, to identify associated manifestations, such as polyphagia (R63.2)
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| UseAdditionalCode |
code to identify body mass index (BMI), if known (Z68.-)
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| E88.89 |
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Other specified metabolic disorders |
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| Launois-Bensaude adenolipomatosis |
| Excludes1 |
adult pulmonary Langerhans cell histiocytosis (J84.82)
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| E88.9 |
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Metabolic disorder, unspecified |
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| E88.A |
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Wasting disease (syndrome) due to underlying condition |
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| Cachexia due to underlying condition |
| CodeFirst |
underlying condition
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| Excludes1 |
cachexia NOS (R64)
nutritional marasmus (E41)
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| Excludes2 |
failure to thrive (R62.51, R62.7)
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