|  D47 |  | Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue   | 
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		|  D47.0 |  | Mast cell neoplasms of uncertain behavior |  
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		| Excludes1 | congenital cutaneous mastocytosis (Q82.2) histiocytic neoplasms of uncertain behavior (D47.Z9)
 malignant mast cell neoplasm (C96.2-)
 
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		|  D47.01 |  | Cutaneous mastocytosis |  
		|  |  | 
| Diffuse cutaneous mastocytosis |  | Maculopapular cutaneous mastocytosis |  | Solitary mastocytoma |  | Telangiectasia macularis eruptiva perstans |  | Urticaria pigmentosa |  
		| Excludes1 | congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2) congenital urticaria pigmentosa (Q82.2)
 extracutaneous mastocytoma (D47.09)
 
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		|  D47.02 |  | Systemic mastocytosis |  
		|  |  | 
| Indolent systemic mastocytosis |  | Isolated bone marrow mastocytosis |  | Smoldering systemic mastocytosis |  | Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD) |  
		| CodeAlso | , if applicable, any associated hematological non-mast cell lineage disease, such as: acute myeloid leukemia (C92.6-, C92.A-)
 chronic myelomonocytic leukemia (C93.1-)
 essential thrombocytosis (D47.3)
 hypereosinophilic syndrome (D72.1)
 myelodysplastic syndrome (D46.9)
 myeloproliferative syndrome (D47.1)
 non-Hodgkin lymphoma (C82-C85)
 plasma cell myeloma (C90.0-)
 polycythemia vera (D45)
 
 |  
		| Excludes1 | aggressive systemic mastocytosis (C96.21) mast cell leukemia (C94.3-)
 
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		|  D47.09 |  | Other mast cell neoplasms of uncertain behavior |  
		|  |  | 
| Extracutaneous mastocytoma |  | Mast cell tumor NOS |  | Mastocytoma NOS |  | Mastocytosis NOS |  |  |  | 
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		|  D47.1 |  | Chronic myeloproliferative disease |  
		|  |  | 
| Chronic neutrophilic leukemia |  | Myeloproliferative disease, unspecified |  
		| Excludes1 | atypical chronic myeloid leukemia BCR/ABL-negative (C92.2-) chronic myeloid leukemia BCR/ABL-positive (C92.1-)
 myelofibrosis NOS (D75.81)
 myelophthisic anemia (D61.82)
 myelophthisis (D61.82)
 secondary myelofibrosis NOS (D75.81)
 
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		|  D47.2 |  | Monoclonal gammopathy |  
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| Monoclonal gammopathy of undetermined significance [MGUS] |  |  | 
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		|  D47.3 |  | Essential (hemorrhagic) thrombocythemia |  
		|  |  | 
| Essential thrombocytosis |  | Idiopathic hemorrhagic thrombocythemia |  | Primary thrombocytosis |  
		| Excludes2 | reactive thrombocytosis (D75.838) secondary thrombocytosis (D75.838)
 thrombocythemia NOS (D75.839)
 thrombocytosis NOS (D75.839)
 
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		|  D47.4 |  | Osteomyelofibrosis |  
		|  |  | 
| Chronic idiopathic myelofibrosis |  | Myelofibrosis (idiopathic) (with myeloid metaplasia) |  | Myelosclerosis (megakaryocytic) with myeloid metaplasia |  | Secondary myelofibrosis in myeloproliferative disease |  
		| Excludes1 | acute myelofibrosis (C94.4-) 
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		|  D47.Z |  | Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue |  |  |  | 
	
		|  D47.Z1 |  | Post-transplant lymphoproliferative disorder (PTLD) |  
		|  |  | 
	
		| CodeFirst | complications of transplanted organs and tissue (T86.-) 
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		| nonPrimary | Yes 
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		|  D47.Z2 |  | Castleman disease |  
		|  |  | 
	
		| CodeAlso | , if applicable, human herpesvirus 8 infection (B10.89) 
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		| Excludes2 | Kaposi's sarcoma (C46.-) 
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		|  D47.Z9 |  | Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue |  
		|  |  | 
| Histiocytic tumors of uncertain behavior |  |  |  | 
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		|  D47.9 |  | Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified |  
		|  |  | 
| Lymphoproliferative disease NOS |  |  |