|  J84 |  | Other interstitial pulmonary diseases   | 
	
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		| CodeAlso | , if applicable, associated condition 
 |  
		| Excludes1 | drug-induced interstitial lung disorders (J70.2-J70.4) interstitial emphysema (J98.2)
 
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		| Excludes2 | lung diseases due to external agents (J60-J70) 
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|  |  | 
	
		|  J84.0 |  | Alveolar and parieto-alveolar conditions |  |  |  | 
	
		|  J84.01 |  | Alveolar proteinosis |  |  |  |  | 
	
		|  J84.02 |  | Pulmonary alveolar microlithiasis |  |  |  |  | 
	
		|  J84.03 |  | Idiopathic pulmonary hemosiderosis |  
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| Essential brown induration of lung |  
		| CodeFirst | underlying disease, such as: disorders of iron metabolism (E83.1-)
 
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		| Excludes1 | acute idiopathic pulmonary hemorrhage in infants [AIPHI] (R04.81) 
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		| nonPrimary | Yes 
 |  |  |  |  |  | 
	
		|  J84.09 |  | Other alveolar and parieto-alveolar conditions |  |  | 
|  |  | 
	
		|  J84.1 |  | Other interstitial pulmonary diseases with fibrosis |  
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		| CodeAlso | , if applicable, pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4) 
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		| Excludes1 | pulmonary fibrosis (chronic) following radiation (J70.1) 
 |  |  |  |  | 
	
		|  J84.10 |  | Pulmonary fibrosis, unspecified |  
		|  |  | 
| Capillary fibrosis of lung |  | Cirrhosis of lung (chronic) NOS |  | Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS |  | Induration of lung (chronic) NOS |  | Postinflammatory pulmonary fibrosis |  |  |  |  |  | 
	
		|  J84.11 |  | Idiopathic interstitial pneumonia |  
		|  |  | 
	
		| Excludes1 | lymphoid interstitial pneumonia (J84.2) pneumocystis pneumonia (B59)
 
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		|  J84.111 |  | Idiopathic interstitial pneumonia, not otherwise specified |  |  |  |  | 
	
		|  J84.112 |  | Idiopathic pulmonary fibrosis |  
		|  |  | 
| Cryptogenic fibrosing alveolitis |  | Idiopathic fibrosing alveolitis |  |  |  |  |  | 
	
		|  J84.113 |  | Idiopathic non-specific interstitial pneumonitis |  
		|  |  | 
	
		| Excludes1 | non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89) 
 |  |  |  |  |  | 
	
		|  J84.114 |  | Acute interstitial pneumonitis |  
		|  |  | 
| Hamman-Rich syndrome |  
		| Excludes1 | pneumocystis pneumonia (B59) 
 |  |  |  |  |  | 
	
		|  J84.115 |  | Respiratory bronchiolitis interstitial lung disease |  |  |  |  | 
	
		|  J84.116 |  | Cryptogenic organizing pneumonia |  
		|  |  | 
	
		| Excludes1 | organizing pneumonia NOS, or due to known underlying cause (J84.89) 
 |  |  |  |  |  | 
	
		|  J84.117 |  | Desquamative interstitial pneumonia |  |  |  |  |  | 
	
		|  J84.17 |  | Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere |  
		|  |  |  |  |  |  | 
	
		|  J84.170 |  | Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere |  
		|  |  | 
| Progressive fibrotic interstitial lung disease |  
		| CodeFirst | underlying disease, such as: lung diseases due to external agents (J60-J70)
 rheumatoid arthritis (M05.00-M06.9)
 sarcoidosis (D86.-)
 systemic connective tissue disorders (M30-M36)
 
 |  |  |  |  |  | 
	
		|  J84.178 |  | Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere |  
		|  |  | 
| Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease |  | Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere |  | Organizing pneumonia due to collagen vascular disease |  | Organizing pneumonia in diseases classified elsewhere |  
		| CodeFirst | underlying disease, such as: progressive systemic sclerosis (M34.0)
 rheumatoid arthritis (M05.00-M06.9)
 systemic lupus erythematosis (M32.0-M32.9)
 
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|  |  | 
	
		|  J84.2 |  | Lymphoid interstitial pneumonia |  
		|  |  | 
| Lymphoid interstitial pneumonitis |  |  | 
|  |  | 
	
		|  J84.8 |  | Other specified interstitial pulmonary diseases |  
		|  |  | 
	
		| Excludes1 | exogenous lipoid pneumonia (J69.1) unspecified lipoid pneumonia (J69.1)
 
 |  |  |  |  | 
	
		|  J84.81 |  | Lymphangioleiomyomatosis |  
		|  |  |  |  |  |  |  | 
	
		|  J84.82 |  | Adult pulmonary Langerhans cell histiocytosis |  
		|  |  | 
| Adult PLCH |  
		| age | Adult: [15-124] 
 |  |  |  |  |  | 
	
		|  J84.83 |  | Surfactant mutations of the lung |  |  |  |  | 
	
		|  J84.84 |  | Other interstitial lung diseases of childhood |  |  |  | 
	
		|  J84.841 |  | Neuroendocrine cell hyperplasia of infancy |  |  |  |  | 
	
		|  J84.842 |  | Pulmonary interstitial glycogenosis |  |  |  |  | 
	
		|  J84.843 |  | Alveolar capillary dysplasia with vein misalignment |  |  |  |  | 
	
		|  J84.848 |  | Other interstitial lung diseases of childhood |  |  |  |  |  | 
	
		|  J84.89 |  | Other specified interstitial pulmonary diseases |  
		|  |  | 
| Endogenous lipoid pneumonia |  | Interstitial pneumonitis |  | Non-specific interstitial pneumonitis NOS |  | Organizing pneumonia NOS |  
		| CodeFirst | , if applicable: poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
 underlying cause of pneumonopathy, if known
 
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		| UseAdditionalCode | code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced 
 |  
		| Excludes1 | cryptogenic organizing pneumonia (J84.116) idiopathic non-specific interstitial pneumonitis (J84.113)
 lipoid pneumonia, exogenous or unspecified (J69.1)
 lymphoid interstitial pneumonia (J84.2)
 
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|  |  | 
	
		|  J84.9 |  | Interstitial pulmonary disease, unspecified |  
		|  |  | 
| Interstitial pneumonia NOS |  |  |