|  Q23 |  | Congenital malformations of aortic and mitral valves   | 
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		|  Q23.0 |  | Congenital stenosis of aortic valve |  
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| Congenital aortic atresia |  | Congenital aortic stenosis NOS |  
		| Excludes1 | congenital stenosis of aortic valve in hypoplastic left heart syndrome (Q23.4) congenital subaortic stenosis (Q24.4)
 supravalvular aortic stenosis (congenital) (Q25.3)
 
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		|  Q23.1 |  | Congenital insufficiency of aortic valve |  
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| Congenital aortic insufficiency |  |  | 
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		|  Q23.2 |  | Congenital mitral stenosis |  
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| Congenital mitral atresia |  |  | 
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		|  Q23.3 |  | Congenital mitral insufficiency |  | 
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		|  Q23.4 |  | Hypoplastic left heart syndrome |  | 
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		|  Q23.8 |  | Other congenital malformations of aortic and mitral valves |  |  |  | 
	
		|  Q23.81 |  | Bicuspid aortic valve |  
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| Congenital bicuspid aortic valve |  | Unicuspid (congenital) aortic valve (at birth) |  
		| CodeAlso | , if applicable, acquired aortic valve disorders, such as: aortic (valve) insufficiency (nonrheumatic) (I35.1)
 aortic (valve) stenosis (nonrheumatic) (I35.0)
 aortic (valve) stenosis with insufficiency (nonrheumatic) (I35.2)
 
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		|  Q23.82 |  | Congenital mitral valve cleft leaflet |  
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| Cleft mitral valve leaflet at birth |  |  |  |  |  | 
	
		|  Q23.88 |  | Other congenital malformations of aortic and mitral valves |  |  | 
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		|  Q23.9 |  | Congenital malformation of aortic and mitral valves, unspecified |  |