ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 9  /  I30-I5A

Other forms of heart disease (I30-I5A)

I30 Acute pericarditis
Includes acute mediastinopericarditis
acute myopericarditis
acute pericardial effusion
acute pleuropericarditis
acute pneumopericarditis
Excludes1 Dressler's syndrome (I24.1)
rheumatic pericarditis (acute) (I01.0)
viral pericarditis due to Coxsakie virus (B33.23)
I30.0 Acute nonspecific idiopathic pericarditis
I30.1 Infective pericarditis
Pneumococcal pericarditis
Pneumopyopericardium
Purulent pericarditis
Pyopericarditis
Pyopericardium
Pyopneumopericardium
Staphylococcal pericarditis
Streptococcal pericarditis
Suppurative pericarditis
Viral pericarditis
UseAdditionalCode code (B95-B97) to identify infectious agent
I30.8 Other forms of acute pericarditis
I30.9 Acute pericarditis, unspecified
I31 Other diseases of pericardium
Excludes1 diseases of pericardium specified as rheumatic (I09.2)
postcardiotomy syndrome (I97.0)
traumatic injury to pericardium (S26.-)
I31.0 Chronic adhesive pericarditis
Accretio cordis
Adherent pericardium
Adhesive mediastinopericarditis
I31.1 Chronic constrictive pericarditis
Concretio cordis
Pericardial calcification
I31.2 Hemopericardium, not elsewhere classified
Excludes1 hemopericardium as current complication following acute myocardial infarction (I23.0)
malignant pericardial effusion (I31.31)
I31.3 Pericardial effusion (noninflammatory)
Excludes1 acute pericardial effusion (I30.9)
I31.31 Malignant pericardial effusion in diseases classified elsewhere
CodeFirst underlying neoplasm (C00-D49)
I31.39 Other pericardial effusion (noninflammatory)
Chylopericardium
I31.4 Cardiac tamponade
CodeFirst underlying cause
nonPrimary Yes
I31.8 Other specified diseases of pericardium
Epicardial plaques
Focal pericardial adhesions
I31.9 Disease of pericardium, unspecified
Pericarditis (chronic) NOS
I32 Pericarditis in diseases classified elsewhere
CodeFirst underlying disease
Excludes1 pericarditis (in):
coxsackie (virus) (B33.23)
gonococcal (A54.83)
meningococcal (A39.53)
rheumatoid (arthritis) (M05.31)
syphilitic (A52.06)
systemic lupus erythematosus (M32.12)
tuberculosis (A18.84)
nonPrimary Yes
I33 Acute and subacute endocarditis
Excludes1 acute rheumatic endocarditis (I01.1)
endocarditis NOS (I38)
I33.0 Acute and subacute infective endocarditis
Bacterial endocarditis (acute) (subacute)
Infective endocarditis (acute) (subacute) NOS
Endocarditis lenta (acute) (subacute)
Malignant endocarditis (acute) (subacute)
Purulent endocarditis (acute) (subacute)
Septic endocarditis (acute) (subacute)
Ulcerative endocarditis (acute) (subacute)
Vegetative endocarditis (acute) (subacute)
UseAdditionalCode code (B95-B97) to identify infectious agent
I33.9 Acute and subacute endocarditis, unspecified
Acute endocarditis NOS
Acute myoendocarditis NOS
Acute periendocarditis NOS
Subacute endocarditis NOS
Subacute myoendocarditis NOS
Subacute periendocarditis NOS
I34 Nonrheumatic mitral valve disorders
Excludes1 mitral valve disease (I05.9)
mitral valve failure (I05.8)
mitral valve stenosis (I05.0)
mitral valve disorder of unspecified cause with diseases of aortic and/or tricuspid valve(s) (I08.-)
mitral valve disorder of unspecified cause with mitral stenosis or obstruction (I05.0)
mitral valve disorder specified as congenital (Q23.2, Q23.9)
mitral valve disorder specified as rheumatic (I05.-)
I34.0 Nonrheumatic mitral (valve) insufficiency
Nonrheumatic mitral (valve) incompetence NOS
Nonrheumatic mitral (valve) regurgitation NOS
CodeAlso , if applicable:
nonrheumatic mitral (valve) annulus calcification (I34.81)
I34.1 Nonrheumatic mitral (valve) prolapse
Floppy nonrheumatic mitral valve syndrome
Excludes1 Marfan's syndrome (Q87.4-)
I34.2 Nonrheumatic mitral (valve) stenosis
CodeAlso , if applicable:
nonrheumatic mitral (valve) annulus calcification (I34.81)
I34.8 Other nonrheumatic mitral valve disorders
I34.81 Nonrheumatic mitral (valve) annulus calcification
Nonrheumatic mitral (valve) annular calcification
Mitral (valve) annulus calcification NOS
CodeAlso , if applicable:
nonrheumatic mitral (valve) insufficiency (I34.0)
nonrheumatic mitral (valve) stenosis (I34.2)
I34.89 Other nonrheumatic mitral valve disorders
I34.9 Nonrheumatic mitral valve disorder, unspecified
I35 Nonrheumatic aortic valve disorders
Excludes1 aortic valve disorder of unspecified cause but with diseases of mitral and/or tricuspid valve(s) (I08.-)
aortic valve disorder specified as congenital (Q23.0, Q23.1)
aortic valve disorder specified as rheumatic (I06.-)
hypertrophic subaortic stenosis (I42.1)
I35.0 Nonrheumatic aortic (valve) stenosis
I35.1 Nonrheumatic aortic (valve) insufficiency
Nonrheumatic aortic (valve) incompetence NOS
Nonrheumatic aortic (valve) regurgitation NOS
I35.2 Nonrheumatic aortic (valve) stenosis with insufficiency
I35.8 Other nonrheumatic aortic valve disorders
I35.9 Nonrheumatic aortic valve disorder, unspecified
I36 Nonrheumatic tricuspid valve disorders
Excludes1 tricuspid valve disorders of unspecified cause (I07.-)
tricuspid valve disorders specified as congenital (Q22.4, Q22.8, Q22.9)
tricuspid valve disorders specified as rheumatic (I07.-)
tricuspid valve disorders with aortic and/or mitral valve involvement (I08.-)
I36.0 Nonrheumatic tricuspid (valve) stenosis
I36.1 Nonrheumatic tricuspid (valve) insufficiency
Nonrheumatic tricuspid (valve) incompetence
Nonrheumatic tricuspid (valve) regurgitation
I36.2 Nonrheumatic tricuspid (valve) stenosis with insufficiency
I36.8 Other nonrheumatic tricuspid valve disorders
I36.9 Nonrheumatic tricuspid valve disorder, unspecified
I37 Nonrheumatic pulmonary valve disorders
Excludes1 pulmonary valve disorder specified as congenital (Q22.1, Q22.2, Q22.3)
pulmonary valve disorder specified as rheumatic (I09.89)
I37.0 Nonrheumatic pulmonary valve stenosis
I37.1 Nonrheumatic pulmonary valve insufficiency
Nonrheumatic pulmonary valve incompetence
Nonrheumatic pulmonary valve regurgitation
I37.2 Nonrheumatic pulmonary valve stenosis with insufficiency
I37.8 Other nonrheumatic pulmonary valve disorders
I37.9 Nonrheumatic pulmonary valve disorder, unspecified
I38 Endocarditis, valve unspecified
Includes endocarditis (chronic) NOS
valvular incompetence NOS
valvular insufficiency NOS
valvular regurgitation NOS
valvular stenosis NOS
valvulitis (chronic) NOS
Excludes1 congenital insufficiency of cardiac valve NOS (Q24.8)
congenital stenosis of cardiac valve NOS (Q24.8)
endocardial fibroelastosis (I42.4)
endocarditis specified as rheumatic (I09.1)
I39 Endocarditis and heart valve disorders in diseases classified elsewhere
CodeFirst underlying disease, such as:
Q fever (A78)
Excludes1 endocardial involvement in:
candidiasis (B37.6)
gonococcal infection (A54.83)
Libman-Sacks disease (M32.11)
listerosis (A32.82)
meningococcal infection (A39.51)
rheumatoid arthritis (M05.31)
syphilis (A52.03)
tuberculosis (A18.84)
typhoid fever (A01.02)
nonPrimary Yes
I40 Acute myocarditis
Includes subacute myocarditis
Excludes1 acute rheumatic myocarditis (I01.2)
I40.0 Infective myocarditis
Septic myocarditis
UseAdditionalCode code (B95-B97) to identify infectious agent
I40.1 Isolated myocarditis
Fiedler's myocarditis
Giant cell myocarditis
Idiopathic myocarditis
I40.8 Other acute myocarditis
I40.9 Acute myocarditis, unspecified
I41 Myocarditis in diseases classified elsewhere
CodeFirst underlying disease, such as:
typhus (A75.0-A75.9)
Excludes1 myocarditis (in):
Chagas' disease (chronic) (B57.2)
acute (B57.0)
coxsackie (virus) infection (B33.22)
diphtheritic (A36.81)
gonococcal (A54.83)
influenzal (J09.X9, J10.82, J11.82)
meningococcal (A39.52)
mumps (B26.82)
rheumatoid arthritis (M05.31)
sarcoid (D86.85)
syphilis (A52.06)
toxoplasmosis (B58.81)
tuberculous (A18.84)
nonPrimary Yes
I42 Cardiomyopathy
Includes myocardiopathy
CodeFirst pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4)
Excludes2 ischemic cardiomyopathy (I25.5)
peripartum cardiomyopathy (O90.3)
ventricular hypertrophy (I51.7)
I42.0 Dilated cardiomyopathy
Congestive cardiomyopathy
I42.1 Obstructive hypertrophic cardiomyopathy
Hypertrophic subaortic stenosis (idiopathic)
I42.2 Other hypertrophic cardiomyopathy
Nonobstructive hypertrophic cardiomyopathy
I42.3 Endomyocardial (eosinophilic) disease
Endomyocardial (tropical) fibrosis
Löffler's endocarditis
I42.4 Endocardial fibroelastosis
Congenital cardiomyopathy
Elastomyofibrosis
I42.5 Other restrictive cardiomyopathy
Constrictive cardiomyopathy NOS
I42.6 Alcoholic cardiomyopathy
CodeAlso presence of alcoholism (F10.-)
I42.7 Cardiomyopathy due to drug and external agent
CodeFirst poisoning due to drug or toxin, if applicable (T36-T65 with fifth or sixth character 1-4)
UseAdditionalCode code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
I42.8 Other cardiomyopathies
I42.9 Cardiomyopathy, unspecified
Cardiomyopathy (primary) (secondary) NOS
I43 Cardiomyopathy in diseases classified elsewhere
CodeFirst underlying disease, such as:
amyloidosis (E85.-)
glycogen storage disease (E74.0-)
gout (M10.0-)
thyrotoxicosis (E05.0-E05.9-)
Excludes1 cardiomyopathy (in):
coxsackie (virus) (B33.24)
diphtheria (A36.81)
sarcoidosis (D86.85)
tuberculosis (A18.84)
nonPrimary Yes
I44 Atrioventricular and left bundle-branch block
I44.0 Atrioventricular block, first degree
I44.1 Atrioventricular block, second degree
Atrioventricular block, type I and II
Möbitz block, type I and II
Second degree block, type I and II
Wenckebach's block
I44.2 Atrioventricular block, complete
Complete heart block NOS
Third degree block
I44.3 Other and unspecified atrioventricular block
Atrioventricular block NOS
I44.30 Unspecified atrioventricular block
I44.39 Other atrioventricular block
I44.4 Left anterior fascicular block
invalidAdmission Yes
I44.5 Left posterior fascicular block
invalidAdmission Yes
I44.6 Other and unspecified fascicular block
I44.60 Unspecified fascicular block
Left bundle-branch hemiblock NOS
invalidAdmission Yes
I44.69 Other fascicular block
invalidAdmission Yes
I44.7 Left bundle-branch block, unspecified
invalidAdmission Yes
I45 Other conduction disorders
I45.0 Right fascicular block
invalidAdmission Yes
I45.1 Other and unspecified right bundle-branch block
I45.10 Unspecified right bundle-branch block
Right bundle-branch block NOS
invalidAdmission Yes
I45.19 Other right bundle-branch block
invalidAdmission Yes
I45.2 Bifascicular block
I45.3 Trifascicular block
I45.4 Nonspecific intraventricular block
Bundle-branch block NOS
I45.5 Other specified heart block
Sinoatrial block
Sinoauricular block
Excludes1 heart block NOS (I45.9)
I45.6 Pre-excitation syndrome
Accelerated atrioventricular conduction
Accessory atrioventricular conduction
Anomalous atrioventricular excitation
Lown-Ganong-Levine syndrome
Pre-excitation atrioventricular conduction
Wolff-Parkinson-White syndrome
I45.8 Other specified conduction disorders
I45.81 Long QT syndrome
I45.89 Other specified conduction disorders
Atrioventricular [AV] dissociation
Interference dissociation
Isorhythmic dissociation
Nonparoxysmal AV nodal tachycardia
I45.9 Conduction disorder, unspecified
Heart block NOS
Stokes-Adams syndrome
I46 Cardiac arrest
Excludes2 cardiogenic shock (R57.0)
I46.2 Cardiac arrest due to underlying cardiac condition
CodeFirst underlying cardiac condition
I46.8 Cardiac arrest due to other underlying condition
CodeFirst underlying condition
I46.9 Cardiac arrest, cause unspecified
I47 Paroxysmal tachycardia
CodeFirst tachycardia complicating:
abortion or ectopic or molar pregnancy (O00-O07, O08.8)
obstetric surgery and procedures (O75.4)
Excludes1 tachycardia NOS (R00.0)
sinoauricular tachycardia NOS (R00.0)
sinus [sinusal] tachycardia NOS (R00.0)
I47.0 Re-entry ventricular arrhythmia
I47.1 Supraventricular tachycardia
I47.10 Supraventricular tachycardia, unspecified
I47.11 Inappropriate sinus tachycardia, so stated
IST
I47.19 Other supraventricular tachycardia
Atrial (paroxysmal) tachycardia
Atrioventricular [AV] (paroxysmal) tachycardia
Atrioventricular re-entrant (nodal) tachycardia [AVNRT] [AVRT]
Junctional (paroxysmal) tachycardia
Nodal (paroxysmal) tachycardia
I47.2 Ventricular tachycardia
I47.20 Ventricular tachycardia, unspecified
I47.21 Torsades de pointes
CodeAlso , if applicable, long QT syndrome (I45.81)
UseAdditionalCode code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
I47.29 Other ventricular tachycardia
I47.9 Paroxysmal tachycardia, unspecified
Bouveret (-Hoffman) syndrome
I48 Atrial fibrillation and flutter
I48.0 Paroxysmal atrial fibrillation
I48.1 Persistent atrial fibrillation
Excludes1 Permanent atrial fibrillation (I48.21)
I48.11 Longstanding persistent atrial fibrillation
I48.19 Other persistent atrial fibrillation
Chronic persistent atrial fibrillation
Persistent atrial fibrillation, NOS
I48.2 Chronic atrial fibrillation
I48.20 Chronic atrial fibrillation, unspecified
Excludes1 Chronic persistent atrial fibrillation (I48.19)
I48.21 Permanent atrial fibrillation
I48.3 Typical atrial flutter
Type I atrial flutter
I48.4 Atypical atrial flutter
Type II atrial flutter
I48.9 Unspecified atrial fibrillation and atrial flutter
I48.91 Unspecified atrial fibrillation
I48.92 Unspecified atrial flutter
I49 Other cardiac arrhythmias
CodeFirst cardiac arrhythmia complicating:
abortion or ectopic or molar pregnancy (O00-O07, O08.8)
obstetric surgery and procedures (O75.4)
Excludes1 neonatal dysrhythmia (P29.1-)
sinoatrial bradycardia (R00.1)
sinus bradycardia (R00.1)
vagal bradycardia (R00.1)
Excludes2 bradycardia NOS (R00.1)
I49.0 Ventricular fibrillation and flutter
I49.01 Ventricular fibrillation
I49.02 Ventricular flutter
I49.1 Atrial premature depolarization
Atrial premature beats
I49.2 Junctional premature depolarization
I49.3 Ventricular premature depolarization
I49.4 Other and unspecified premature depolarization
I49.40 Unspecified premature depolarization
Premature beats NOS
I49.49 Other premature depolarization
Ectopic beats
Extrasystoles
Extrasystolic arrhythmias
Premature contractions
I49.5 Sick sinus syndrome
Tachycardia-bradycardia syndrome
I49.8 Other specified cardiac arrhythmias
Brugada syndrome
Coronary sinus rhythm disorder
Ectopic rhythm disorder
Nodal rhythm disorder
I49.9 Cardiac arrhythmia, unspecified
Arrhythmia (cardiac) NOS
I50 Heart failure
CodeFirst heart failure complicating abortion or ectopic or molar pregnancy (O00-O07, O08.8)
heart failure due to hypertension (I11.0)
heart failure due to hypertension with chronic kidney disease (I13.-)
heart failure following surgery (I97.13-)
obstetric surgery and procedures (O75.4)
rheumatic heart failure (I09.81)
Excludes2 cardiac arrest (I46.-)
neonatal cardiac failure (P29.0)
I50.1 Left ventricular failure, unspecified
Cardiac asthma
Edema of lung with heart disease NOS
Edema of lung with heart failure
Left heart failure
Pulmonary edema with heart disease NOS
Pulmonary edema with heart failure
Excludes1 edema of lung without heart disease or heart failure (J81.-)
pulmonary edema without heart disease or failure (J81.-)
I50.2 Systolic (congestive) heart failure
Heart failure with reduced ejection fraction [HFrEF]
Systolic left ventricular heart failure
CodeAlso end stage heart failure, if applicable (I50.84)
Excludes1 combined systolic (congestive) and diastolic (congestive) heart failure (I50.4-)
I50.20 Unspecified systolic (congestive) heart failure
I50.21 Acute systolic (congestive) heart failure
I50.22 Chronic systolic (congestive) heart failure
I50.23 Acute on chronic systolic (congestive) heart failure
I50.3 Diastolic (congestive) heart failure
Diastolic left ventricular heart failure
Heart failure with normal ejection fraction
Heart failure with preserved ejection fraction [HFpEF]
CodeAlso end stage heart failure, if applicable (I50.84)
Excludes1 combined systolic (congestive) and diastolic (congestive) heart failure (I50.4-)
I50.30 Unspecified diastolic (congestive) heart failure
I50.31 Acute diastolic (congestive) heart failure
I50.32 Chronic diastolic (congestive) heart failure
I50.33 Acute on chronic diastolic (congestive) heart failure
I50.4 Combined systolic (congestive) and diastolic (congestive) heart failure
Combined systolic and diastolic left ventricular heart failure
Heart failure with reduced ejection fraction and diastolic dysfunction
CodeAlso end stage heart failure, if applicable (I50.84)
I50.40 Unspecified combined systolic (congestive) and diastolic (congestive) heart failure
I50.41 Acute combined systolic (congestive) and diastolic (congestive) heart failure
I50.42 Chronic combined systolic (congestive) and diastolic (congestive) heart failure
I50.43 Acute on chronic combined systolic (congestive) and diastolic (congestive) heart failure
I50.8 Other heart failure
I50.81 Right heart failure
Right ventricular failure
I50.810 Right heart failure, unspecified
Right heart failure without mention of left heart failure
Right ventricular failure NOS
I50.811 Acute right heart failure
Acute isolated right heart failure
Acute (isolated) right ventricular failure
I50.812 Chronic right heart failure
Chronic isolated right heart failure
Chronic (isolated) right ventricular failure
I50.813 Acute on chronic right heart failure
Acute on chronic isolated right heart failure
Acute on chronic (isolated) right ventricular failure
Acute decompensation of chronic (isolated) right ventricular failure
Acute exacerbation of chronic (isolated) right ventricular failure
I50.814 Right heart failure due to left heart failure
Right ventricular failure secondary to left ventricular failure
CodeAlso the type of left ventricular failure, if known (I50.2-I50.43)
Excludes1 Right heart failure with but not due to left heart failure (I50.82)
I50.82 Biventricular heart failure
CodeAlso the type of left ventricular failure as systolic, diastolic, or combined, if known (I50.2-I50.43)
I50.83 High output heart failure
I50.84 End stage heart failure
Stage D heart failure
CodeAlso the type of heart failure as systolic, diastolic, or combined, if known (I50.2-I50.43)
I50.89 Other heart failure
I50.9 Heart failure, unspecified
Cardiac, heart or myocardial failure NOS
Congestive heart disease
Congestive heart failure NOS
Excludes2 fluid overload unrelated to congestive heart failure (E87.70)
I51 Complications and ill-defined descriptions of heart disease
Excludes1 any condition in I51.4-I51.9 due to hypertension (I11.-)
any condition in I51.4-I51.9 due to hypertension and chronic kidney disease (I13.-)
heart disease specified as rheumatic (I00-I09)
I51.0 Cardiac septal defect, acquired
Acquired septal atrial defect (old)
Acquired septal auricular defect (old)
Acquired septal ventricular defect (old)
Excludes1 cardiac septal defect as current complication following acute myocardial infarction (I23.1, I23.2)
age Adult: [15-124]
I51.1 Rupture of chordae tendineae, not elsewhere classified
Excludes1 rupture of chordae tendineae as current complication following acute myocardial infarction (I23.4)
I51.2 Rupture of papillary muscle, not elsewhere classified
Excludes1 rupture of papillary muscle as current complication following acute myocardial infarction (I23.5)
I51.3 Intracardiac thrombosis, not elsewhere classified
Apical thrombosis (old)
Atrial thrombosis (old)
Auricular thrombosis (old)
Mural thrombosis (old)
Ventricular thrombosis (old)
Excludes1 intracardiac thrombosis as current complication following acute myocardial infarction (I23.6)
I51.4 Myocarditis, unspecified
Chronic (interstitial) myocarditis
Myocardial fibrosis
Myocarditis NOS
Excludes1 acute or subacute myocarditis (I40.-)
I51.5 Myocardial degeneration
Fatty degeneration of heart or myocardium
Myocardial disease
Senile degeneration of heart or myocardium
I51.7 Cardiomegaly
Cardiac dilatation
Cardiac hypertrophy
Ventricular dilatation
I51.8 Other ill-defined heart diseases
I51.81 Takotsubo syndrome
Reversible left ventricular dysfunction following sudden emotional stress
Stress induced cardiomyopathy
Takotsubo cardiomyopathy
Transient left ventricular apical ballooning syndrome
I51.89 Other ill-defined heart diseases
Carditis (acute)(chronic)
Pancarditis (acute)(chronic)
I51.9 Heart disease, unspecified
I52 Other heart disorders in diseases classified elsewhere
CodeFirst underlying disease, such as:
congenital syphilis (A50.5)
mucopolysaccharidosis (E76.3)
schistosomiasis (B65.0-B65.9)
Excludes1 heart disease (in):
gonococcal infection (A54.83)
meningococcal infection (A39.50)
rheumatoid arthritis (M05.31)
syphilis (A52.06)
nonPrimary Yes
I5A Non-ischemic myocardial injury (non-traumatic)
Acute (non-ischemic) myocardial injury
Chronic (non-ischemic) myocardial injury
Unspecified (non-ischemic) myocardial injury
CodeFirst the underlying cause, if known and applicable, such as:
acute kidney failure (N17.-)
acute myocarditis (I40.-)
cardiomyopathy (I42.-)
chronic kidney disease (CKD) (N18.-)
heart failure (I50.-)
hypertensive urgency (I16.0)
nonrheumatic aortic valve disorders (I35.-)
paroxysmal tachycardia (I47.-)
pulmonary embolism (I26.-)
pulmonary hypertension (I27.0, I27.2-)
sepsis (A41.-)
takotsubo syndrome (I51.81)
Excludes1 acute myocardial infarction (I21.-)
injury of heart (S26.-)
Excludes2 other acute ischemic heart diseases (I24.-)