ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 12  /  L10-L14

Bullous disorders (L10-L14)

Excludes1: benign familial pemphigus [Hailey-Hailey] (Q82.8)
staphylococcal scalded skin syndrome (L00)
toxic epidermal necrolysis [Lyell] (L51.2)
L10 Pemphigus
Excludes1 pemphigus neonatorum (L01.03)
L10.0 Pemphigus vulgaris
L10.1 Pemphigus vegetans
L10.2 Pemphigus foliaceous
L10.3 Brazilian pemphigus [fogo selvagem]
L10.4 Pemphigus erythematosus
Senear-Usher syndrome
L10.5 Drug-induced pemphigus
UseAdditionalCode code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
L10.8 Other pemphigus
L10.81 Paraneoplastic pemphigus
L10.89 Other pemphigus
L10.9 Pemphigus, unspecified
L11 Other acantholytic disorders
L11.0 Acquired keratosis follicularis
Excludes1 keratosis follicularis (congenital) [Darier-White] (Q82.8)
L11.1 Transient acantholytic dermatosis [Grover]
L11.8 Other specified acantholytic disorders
L11.9 Acantholytic disorder, unspecified
L12 Pemphigoid
Excludes1 herpes gestationis (O26.4-)
impetigo herpetiformis (L40.1)
L12.0 Bullous pemphigoid
L12.1 Cicatricial pemphigoid
Benign mucous membrane pemphigoid
L12.2 Chronic bullous disease of childhood
Juvenile dermatitis herpetiformis
age Pediatric: [0-17]
L12.3 Acquired epidermolysis bullosa
Excludes1 epidermolysis bullosa (congenital) (Q81.-)
L12.30 Acquired epidermolysis bullosa, unspecified
L12.31 Epidermolysis bullosa due to drug
UseAdditionalCode code for adverse effect, if applicable, to identify drug (T36-T50 with fifth or sixth character 5)
L12.35 Other acquired epidermolysis bullosa
L12.8 Other pemphigoid
L12.9 Pemphigoid, unspecified
L13 Other bullous disorders
L13.0 Dermatitis herpetiformis
Duhring's disease
Hydroa herpetiformis
Excludes1 juvenile dermatitis herpetiformis (L12.2)
senile dermatitis herpetiformis (L12.0)
L13.1 Subcorneal pustular dermatitis
Sneddon-Wilkinson disease
L13.8 Other specified bullous disorders
L13.9 Bullous disorder, unspecified
L14 Bullous disorders in diseases classified elsewhere
CodeFirst underlying disease
nonPrimary Yes