ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 2  /  D37-D48  /  D47
D47 Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.0 Mast cell neoplasms of uncertain behavior
Excludes1 congenital cutaneous mastocytosis (Q82.2)
histiocytic neoplasms of uncertain behavior (D47.Z9)
malignant mast cell neoplasm (C96.2-)
D47.01 Cutaneous mastocytosis
Diffuse cutaneous mastocytosis
Maculopapular cutaneous mastocytosis
Solitary mastocytoma
Telangiectasia macularis eruptiva perstans
Urticaria pigmentosa
Excludes1 congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
congenital urticaria pigmentosa (Q82.2)
extracutaneous mastocytoma (D47.09)
D47.02 Systemic mastocytosis
Indolent systemic mastocytosis
Isolated bone marrow mastocytosis
Smoldering systemic mastocytosis
Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)
CodeAlso , if applicable, any associated hematological non-mast cell lineage disease, such as:
acute myeloid leukemia (C92.6-, C92.A-)
chronic myelomonocytic leukemia (C93.1-)
essential thrombocytosis (D47.3)
hypereosinophilic syndrome (D72.1)
myelodysplastic syndrome (D46.9)
myeloproliferative syndrome (D47.1)
non-Hodgkin lymphoma (C82-C85)
plasma cell myeloma (C90.0-)
polycythemia vera (D45)
Excludes1 aggressive systemic mastocytosis (C96.21)
mast cell leukemia (C94.3-)
D47.09 Other mast cell neoplasms of uncertain behavior
Extracutaneous mastocytoma
Mast cell tumor NOS
Mastocytoma NOS
Mastocytosis NOS
D47.1 Chronic myeloproliferative disease
Chronic neutrophilic leukemia
Myeloproliferative disease, unspecified
Excludes1 atypical chronic myeloid leukemia BCR/ABL-negative (C92.2-)
chronic myeloid leukemia BCR/ABL-positive (C92.1-)
myelofibrosis NOS (D75.81)
myelophthisic anemia (D61.82)
myelophthisis (D61.82)
secondary myelofibrosis NOS (D75.81)
D47.2 Monoclonal gammopathy
Monoclonal gammopathy of undetermined significance [MGUS]
D47.3 Essential (hemorrhagic) thrombocythemia
Essential thrombocytosis
Idiopathic hemorrhagic thrombocythemia
Primary thrombocytosis
Excludes2 reactive thrombocytosis (D75.838)
secondary thrombocytosis (D75.838)
thrombocythemia NOS (D75.839)
thrombocytosis NOS (D75.839)
D47.4 Osteomyelofibrosis
Chronic idiopathic myelofibrosis
Myelofibrosis (idiopathic) (with myeloid metaplasia)
Myelosclerosis (megakaryocytic) with myeloid metaplasia
Secondary myelofibrosis in myeloproliferative disease
Excludes1 acute myelofibrosis (C94.4-)
D47.Z Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
D47.Z1 Post-transplant lymphoproliferative disorder (PTLD)
CodeFirst complications of transplanted organs and tissue (T86.-)
nonPrimary Yes
D47.Z2 Castleman disease
CodeAlso , if applicable, human herpesvirus 8 infection (B10.89)
Excludes2 Kaposi's sarcoma (C46.-)
D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
Histiocytic tumors of uncertain behavior
D47.9 Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified
Lymphoproliferative disease NOS