ICD-10-CM Book 2024 Edition

Chapters  /  Chapter 3  /  D65-D69

Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)

D65 Disseminated intravascular coagulation [defibrination syndrome]
Afibrinogenemia, acquired
Consumption coagulopathy
COVID-19 associated diffuse or disseminated intravascular coagulopathy
Diffuse or disseminated intravascular coagulation [DIC]
Fibrinolytic hemorrhage, acquired
Fibrinolytic purpura
Purpura fulminans
CodeAlso , if applicable, associated condition
Excludes1 disseminated intravascular coagulation (complicating):
abortion or ectopic or molar pregnancy (O00-O07, O08.1)
in newborn (P60)
pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
D66 Hereditary factor VIII deficiency
Classical hemophilia
Deficiency factor VIII (with functional defect)
Hemophilia NOS
Hemophilia A
Excludes1 factor VIII deficiency with vascular defect (D68.0-)
D67 Hereditary factor IX deficiency
Christmas disease
Factor IX deficiency (with functional defect)
Hemophilia B
Plasma thromboplastin component [PTC] deficiency
D68 Other coagulation defects
Excludes1 abnormal coagulation profile NOS (R79.1)
Excludes2 coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
D68.0 Von Willebrand disease
Excludes1 capillary fragility (hereditary) (D69.8)
factor VIII deficiency NOS (D66)
factor VIII deficiency with functional defect (D66)
D68.00 Von Willebrand disease, unspecified
D68.01 Von Willebrand disease, type 1
Partial quantitative deficiency of von Willebrand factor
Type 1C von Willebrand disease
D68.02 Von Willebrand disease, type 2
Qualitative defects of von Willebrand factor
D68.020 Von Willebrand disease, type 2A
Qualitative defects of von Willebrand factor with decreased platelet adhesion and selective deficiency of high-molecular-weight multimers
D68.021 Von Willebrand disease, type 2B
Qualitative defects of von Willebrand factor with high-molecular-weight von Willebrand factor loss
Qualitative defects of von Willebrand factor with hyper-adhesive forms
Qualitative defects of von Willebrand factor with increased affinity for platelet glycoprotein lb
D68.022 Von Willebrand disease, type 2M
Qualitative defects of von Willebrand factor with defective platelet adhesion with a normal size distribution of von Willebrand factor multimers
D68.023 Von Willebrand disease, type 2N
Qualitative defects of von Willebrand factor with defective von Willebrand factor to factor VIII binding
Qualitative defects of von Willebrand factor with markedly decreased affinity for factor VIII
D68.029 Von Willebrand disease, type 2, unspecified
Qualitative defect in von Willebrand factor function, with no further subtyping
D68.03 Von Willebrand disease, type 3
(Near) complete absence of von Willebrand factor
Total quantitative deficiency of von Willebrand factor
D68.04 Acquired von Willebrand disease
Acquired von Willebrand syndrome
D68.09 Other von Willebrand disease
Platelet-type von Willebrand disease
Pseudo-von Willebrand disease
CodeAlso , if applicable, qualitative platelet defects (D69.1)
D68.1 Hereditary factor XI deficiency
Hemophilia C
Plasma thromboplastin antecedent [PTA] deficiency
Rosenthal's disease
D68.2 Hereditary deficiency of other clotting factors
AC globulin deficiency
Congenital afibrinogenemia
Deficiency of factor I [fibrinogen]
Deficiency of factor II [prothrombin]
Deficiency of factor V [labile]
Deficiency of factor VII [stable]
Deficiency of factor X [Stuart-Prower]
Deficiency of factor XII [Hageman]
Deficiency of factor XIII [fibrin stabilizing]
Dysfibrinogenemia (congenital)
Hypoproconvertinemia
Owren's disease
Proaccelerin deficiency
D68.3 Hemorrhagic disorder due to circulating anticoagulants
D68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.311 Acquired hemophilia
Autoimmune hemophilia
Autoimmune inhibitors to clotting factors
Secondary hemophilia
D68.312 Antiphospholipid antibody with hemorrhagic disorder
Lupus anticoagulant (LAC) with hemorrhagic disorder
Systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder
Excludes1 antiphospholipid antibody, finding without diagnosis (R76.0)
antiphospholipid antibody syndrome (D68.61)
antiphospholipid antibody with hypercoagulable state (D68.61)
lupus anticoagulant (LAC) finding without diagnosis (R76.0)
lupus anticoagulant (LAC) with hypercoagulable state (D68.62)
systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.62)
D68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
Antithromboplastinemia
Antithromboplastinogenemia
Hemorrhagic disorder due to intrinsic increase in antithrombin
Hemorrhagic disorder due to intrinsic increase in anti-VIIIa
Hemorrhagic disorder due to intrinsic increase in anti-IXa
Hemorrhagic disorder due to intrinsic increase in anti-XIa
D68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulants
Drug-induced hemorrhagic disorder
Hemorrhagic disorder due to increase in anti-IIa
Hemorrhagic disorder due to increase in anti-Xa
Hyperheparinemia
UseAdditionalCode code for adverse effect, if applicable, to identify drug (T45.515, T45.525)
D68.4 Acquired coagulation factor deficiency
Deficiency of coagulation factor due to liver disease
Deficiency of coagulation factor due to vitamin K deficiency
Excludes1 vitamin K deficiency of newborn (P53)
D68.5 Primary thrombophilia
Primary hypercoagulable states
Excludes1 antiphospholipid syndrome (D68.61)
lupus anticoagulant (D68.62)
secondary activated protein C resistance (D68.69)
secondary antiphospholipid antibody syndrome (D68.69)
secondary lupus anticoagulant with hypercoagulable state (D68.69)
secondary systemic lupus erythematosus [SLE] inhibitor with hypercoagulable state (D68.69)
systemic lupus erythematosus [SLE] inhibitor finding without diagnosis (R76.0)
systemic lupus erythematosus [SLE] inhibitor with hemorrhagic disorder (D68.312)
thrombotic thrombocytopenic purpura (M31.19)
D68.51 Activated protein C resistance
Factor V Leiden mutation
D68.52 Prothrombin gene mutation
D68.59 Other primary thrombophilia
Antithrombin III deficiency
Hypercoagulable state NOS
Primary hypercoagulable state NEC
Primary thrombophilia NEC
Protein C deficiency
Protein S deficiency
Thrombophilia NOS
D68.6 Other thrombophilia
Other hypercoagulable states
Excludes1 diffuse or disseminated intravascular coagulation [DIC] (D65)
heparin induced thrombocytopenia (HIT) (D75.82-)
hyperhomocysteinemia (E72.11)
D68.61 Antiphospholipid syndrome
Anticardiolipin syndrome
Antiphospholipid antibody syndrome
Excludes1 anti-phospholipid antibody, finding without diagnosis (R76.0)
anti-phospholipid antibody with hemorrhagic disorder (D68.312)
lupus anticoagulant syndrome (D68.62)
D68.62 Lupus anticoagulant syndrome
Lupus anticoagulant
Presence of systemic lupus erythematosus [SLE] inhibitor
Excludes1 anticardiolipin syndrome (D68.61)
antiphospholipid syndrome (D68.61)
lupus anticoagulant (LAC) finding without diagnosis (R76.0)
lupus anticoagulant (LAC) with hemorrhagic disorder (D68.312)
D68.69 Other thrombophilia
COVID-19 associated hypercoagulability
Hypercoagulable states NEC
Secondary hypercoagulable state NOS
CodeAlso , if applicable, associated condition
D68.8 Other specified coagulation defects
COVID-19 associated coagulopathy
CodeAlso , if applicable, associated condition
Excludes1 hemorrhagic disease of newborn (P53)
D68.9 Coagulation defect, unspecified
D69 Purpura and other hemorrhagic conditions
Excludes1 benign hypergammaglobulinemic purpura (D89.0)
cryoglobulinemic purpura (D89.1)
essential (hemorrhagic) thrombocythemia (D47.3)
hemorrhagic thrombocythemia (D47.3)
purpura fulminans (D65)
thrombotic thrombocytopenic purpura (M31.19)
Waldenström hypergammaglobulinemic purpura (D89.0)
D69.0 Allergic purpura
Allergic vasculitis
Nonthrombocytopenic hemorrhagic purpura
Nonthrombocytopenic idiopathic purpura
Purpura anaphylactoid
Purpura Henoch(-Schönlein)
Purpura rheumatica
Vascular purpura
Excludes1 thrombocytopenic hemorrhagic purpura (D69.3)
D69.1 Qualitative platelet defects
Bernard-Soulier [giant platelet] syndrome
Glanzmann's disease
Grey platelet syndrome
Thromboasthenia (hemorrhagic) (hereditary)
Thrombocytopathy
Excludes1 hemolytic-uremic syndrome (D59.3-)
Excludes2 von Willebrand disease (D68.0-)
D69.2 Other nonthrombocytopenic purpura
Purpura NOS
Purpura simplex
Senile purpura
D69.3 Immune thrombocytopenic purpura
Hemorrhagic (thrombocytopenic) purpura
Idiopathic thrombocytopenic purpura
Tidal platelet dysgenesis
D69.4 Other primary thrombocytopenia
Excludes1 transient neonatal thrombocytopenia (P61.0)
Wiskott-Aldrich syndrome (D82.0)
D69.41 Evans syndrome
D69.42 Congenital and hereditary thrombocytopenia purpura
Congenital thrombocytopenia
Hereditary thrombocytopenia
CodeFirst congential or hereditary disorder, such as:
thrombocytopenia with absent radius (TAR syndrome) (Q87.2)
D69.49 Other primary thrombocytopenia
Megakaryocytic hypoplasia
Primary thrombocytopenia NOS
D69.5 Secondary thrombocytopenia
Excludes1 heparin induced thrombocytopenia (HIT) (D75.82-)
transient thrombocytopenia of newborn (P61.0)
D69.51 Posttransfusion purpura
Posttransfusion purpura from whole blood (fresh) or blood products
PTP
D69.59 Other secondary thrombocytopenia
D69.6 Thrombocytopenia, unspecified
D69.8 Other specified hemorrhagic conditions
Capillary fragility (hereditary)
Vascular pseudohemophilia
D69.9 Hemorrhagic condition, unspecified